Impilo, Izifo nemibandela
Vasculitis loluhleliwe: izimpawu kanye nokwelashwa. Vasculitis - Siyini ngempela lesi sifo?
Vasculitis - Siyini ngempela lesi sifo futhi kanjani eziyinkimbinkimbi ezithinta umzimba kulesi simo?
isifo semithambo
imithambo yegazi ngenxa izici ezihlukahlukene ezimbi bangase balahlekelwe umsebenzi wabo, esithinta isimo wonke umzimba.
vasculitis lefundo - izifo okuyizinto ezihlobene izindonga normal semithambo. Ngesikhathi sigaba abakhona izinhlobo eziningana lesi sifo.
Amafomu yesifo letindzala
zinhlobo Akwaziwa izinguquko semithambo sokugembula:
- Ukunqotshwa kwe-amasegimenti ngazinye medium imithambo noma esincane okuthiwa periarthritis nodosa.
- Izifo esithinta ngokuyinhloko imithambo nemithambo yegazi ipheshana zokuphefumula namaphaphu, nezinso kuphela ke, kuchazwa njenganoma granulomatosis Wegener sika.
- vasculitis lefundo, ogama izimpawu zibonisa zokugula izitsha enkulu umzimba (avame - imithambo ikhanda), ngokuthi cell giant arteritis yesikhashana.
- izinqubo ukuvuvukala kule imithambo esikhulu elikuyi-aorta kuchazwa njengoba isifo Takayasu, noma aortoarteriit nonspecific.
- Ngokuqondene zokugula of kwemisipha hlobo imithambo ke lesi sifo kuchazwa njenganoma thromboangiitis obliterans.
- isifo lefundo okuyinto kuhambisana izimpawu ezifana stomatitis, a izicubu lesion emlonyeni mucosa zangasese, kanye noshintsho iso liye labizwa ngokuthi "Behcet Syndrome."
- vasculitis nomzimba.
Zonke izinhlobo ngenhla ezihlobene nokusebenzelana izimbangela ezithile ukuthi kuphakamisa izinguquko Imithambo yegazi kanye nokwephula imisebenzi yabo.
Izimbangela zesifo
Ukuze sithole intuthuko ukwelashwa okunengqondo nezindlela zokuzivikela, kubalulekile ukwazi ukuthi yini ebangela lokhu noma lokhuya izinguquko sokugembula imithambo. Esimweni esinjalo, vasculitis letindzala angase abe umphumela omuhle ukuze isiguli.
Hhayi balitadishisise zonke izici ukuthi avuse lesi sifo, kodwa izizathu ezimbalwa ezenza kungenzeka bathi:
- vasculitis lefundo njengoba endleleni umzimba osabela ngayo ukuba ukusetshenziswa kunemithi noma amaphilisi owaphuzayo. izinguquko sokugembula isitsha izindonga Ungase futhi avuse isifo yegciwane osekuyisikhathi eside idelela ukwelashwa.
- vasculitis lefundo njengoba inkinga kwezinye izifo nolaka ezithathelwanayo zidluliselwe.
- imithambo yegazi zingadilizwa ngesikhathi izifo ezifana nesifo sokuqaqamba kwamalunga esisheshayo, omzimba izicubu erythematosus, izinqubo ukuvuvukala kule ndlala, ezingamahlalakhona pathologies sokuhlasela kwamasosha omzimba, Schwartz-Jampel syndrome, futhi ngezinye izikhathi glomerulonephritis.
Zonke lezi zici ukucacisa vasculitis letindzala. Izimpawu nasekwelashweni kwezifo kungakephuzi akuyona njalo exhumene, ngoba ezinye izenzo lesi sifo yilabo ifomu esicashile, kuyilapho abanye, Ngakolunye uhlangothi, baphokophelele ukungena ngemvume uphethwe okungalungile.
Kwenzekani emzimbeni? pathogenesis
I zokugula we isimiso semithambo yegazi kuhilelani izinguquko eziyingozi emzimbeni, okuyinto ziboniswa emazingeni ahlukahlukeneko wendlela isifo. Iphuzu liwukuthi ukuthi ezitsheni ithumba ukuvuvukala nokubhujiswa alandelayo izindonga zawo.
Uhlobo ngalunye vasculitis ethulwa ukuqhutshwa izici zayo siqu.
Iziphi izinguquko kuhambisana yonke inhlobo?
- Lapho syndrome Behcet waphawula izimpawu kule ngalo ingaphakathi ngomlomo, e stomatitis ethile, ophuma kanye ukwehluleka kwesikhashana. Ingxenye yesibili uphawu kungenziwa ngokuthi ulcer scrotum in abesilisa nabesifazane - e sangasese futhi ngemomozi yakho. Ngaphezu kwalokho mucosa, lolu hlobo vasculitis ngezindlela ezingafani kuthinta zamehlo.
- Thromboangiitis obliterans kuhambisana izikhalazo zeziguli, ukuthuthukiswa izinyonga noma ukuba ndikindiki okungazelelwe izandla.
- Aortoarteriit unika imiphumela nonspecific ezifana ubuhlungu kule aphansi kanye engenhla emikhawulweni, iqolo, onikelwa esiswini, kanye nokuquleka neziyaluyalu ezihlobene amehlo.
Ezinye izinhlobo, kuye ngobucayi, cishe izimpawu ezifanayo, kodwa zidinga indlela ngamunye ekwelashweni.
lingaze isithombe
Symptomatology isifo semithambo Ungashintsha isithombe sakho, kuye ngokuthi yini inqubo kwasendaweni kanye pathologies ukuthi ngihambe nabo.
Vasculitis imbangela ukuqubuka, neziyaluyalu sokugembula e isimiso sezinzwa kuhilelani ukuzwela, okuyinto ingase ihluke hypersensitivity kuya ukuzwela ongaphakeme noma ukungabi wako anda.
Lapho kunyatheliswa igazi izitsha ubuchopho, kungenzeka kukhona yokufa uhlangothi nokumelwa yinhliziyo. vasculitis Allergic sinezimfanelo njengoba ejwayelekile nge ukusabela iguliswa umfutho.
Izimpawu zokugula semithambo
Kukhona izimpawu ezithile ezivamile yiluphi uhlobo vasculitis yilesi:
- ukulahlekelwa esinqunyiwe noma ephelele ukudla;
- ubuthakathaka umzimba okubonakala ngaphandle kwesizathu, futhi kuhambisana nokunganaki;
- ukukhathala okusheshayo, ngokomzimba nangokokuziphatha;
- isigqugquzeli lokushisa komzimba - ongaphakeme-ebangeni, ngezinye izikhathi kuphela kuziwa febrile;
- isikhumba ugodo, ehambisana ne-ukwephulwa kwegazi jikelele emzimbeni.
Yini enye okwesikhathi vasculitis letindzala? Siyini ngempela lesi sifo futhi kanjani ukumelana naso, kungatholakala ezinye izici ezivamile. Ngokwesibonelo, hlobo nodular ka vasculitis wabonakaliswa imisipha ezidabukile wonke umzimba. Ubuhlungu kudlulela esiswini, avuse kwesisindo, iziyaluyalu emathunjini, ukuhlanza, isicanucanu futhi ngikhishwe, ngenxa yalokho, okuthile engqondweni.
granulomatosis Wegner sika, kuphakamisa isifo ingaphakathi acinene, noma ngaphezulu ngokunembile, esifubeni yayo - ubomvu, igazi isikhwehlela. izinqubo esidalwa yizilonda emathunjini sibe kungenzeka le mucosa acinene. Khona-ke kukhwehlela kwenzeka, ubuhlungu besifuba, iphika, ukungasebenzi kwezinso nabanye.
izilonda
Lapho izinqubo sokugembula izitsha kubangelwa ukusabela iguliswa ke lolu hlobo vasculitis ngokuthi isikhumba. Injani vasculitis isikhumba?
Emelelwa sifo has izinhlobo eziningana ukugeleza:
- uhlobo lokuqala - nodosa necrotic noma Werther-Dyumlinga owabonakaliswa dermal amasayithi umbala wesikhumba nge bluish umthunzi brown;
- yesibili - arteriollit iguliswa Ruiter, esizibonakalisa ejwayelekile eritrematoznymi ukuqubuka esikhumbeni, kanye oluhambisana soma, izilonda, erosions nge necrosis okwalandela.
Ukuxilongwa letindzala isifo semithambo
Kukhethwa izindlela zokuxilonga kufanele esekelwe ukubonakaliswa sangaphandle vasculitis, kodwa ukunquma buyisiphi ofihlekile asesebenzisa letengetiwe kulolu cwaningo.
Ukuqala isiguli okungahle kwenzeke, kufanele uhlolwe igazi ukucacisa ushintsho wakhe. Lapho izinkomba ambalwa of-hemoglobin kakhulu lingaphansi kunalokhu okujwayelekile, lokho kubonisa ekuqaleni izinqubo anemiya emzimbeni - isimo esibucayi zokugula semithambo.
Akuvamile, kodwa kwenzeka lapho uphethwe "vasculitis letindzala" ibekwe ngesisekelo ukuhlaziywa umchamo, uma ukuthola amangqamuzana abomvu igazi amangqamuzana amhlophe egazi.
Eyesibili Assay value, kodwa hhayi ngaphansi ezibalulekile Ihlahlubo, biopsy. Kuze kube yimanje, isiguli luhlolo ezincane kufanele athathe ingxenye izicubu isitsha.
vasculitis lefundo. Izimpawu kanye Ukwelashwa
Kuye kungaba vasculitis iguliswa noma ukwelashwa yesibili ezinqunyiwe ngamunye, futhi iqondiswa hhayi kuphela ekwelapheni isifo esithile ngokuqondile, kodwa futhi wokubuyiselwa kwayo yonke indikimba, okuyinto yabhidlika kabana lapho ngemuva zokugula semithambo.
Umgomo kwelashwa nokuqedwa ephelele izimpawu zesifo, ukuzinza imithambo yegazi kanye ukuzungeza.
Izidakamizwa ukuthi ziyasebenza e vasculitis letindzala:
- imithi ngama-corticosteroid;
- ejenti chemotherapeutic;
- immunosuppressants.
Lapho nolaka vasculitis ezidingekayo ukuqhuba labagula kakhulu kanye nokwelashwa. Lokhu kuyadingeka uma ukungasebenzi izitho ezibalulekile ezifana inhliziyo, isibindi, amaphaphu nezinso. Kulokhu, a yokusiza umuntu ukuba aphefumule nesineke kulandele ukuphathwa lingaze.
isikhumba vasculitis ezidingekayo yokwelapha sinenkonzo yokunakekela iziguli emakhaya noma esibhedlela, kuncike progressiveness yenqubo sokugembula. Liphumelele kule isifo kuyoba umthelela yokulungiswa olukhulu isayithi ukutheleleka, okuyinto eyenzeka kakade esigabeni ezingamahlalakhona.
Isiguli kufanele ilandelwe nge embhedeni ukuphumula nokuthatha imithi ezilandelayo:
- antihistamine, kuhlanganise imithi ephumelelayo vasculitis kukhona "Promethazine", "Diphenhydramine", "Fenkarol";
- calcium amalungiselelo microelement - 10% i-calcium chloride umjovo noma isixazululo gluconate;
- rutin, ascorbic acid.
Lapho nokungasebenzi zisebenza ukwelashwa eyinkimbinkimbi ngokusebenzisa amalungiselelo hormone ezifana nemithi "prednisolone" futhi "Dexamethasone".
Lapho lesi sifo kuhambisana isilonda nezinqubo necrotic, ukuphathwa kuhlanganisa isicelo ngezihloko ezihlukene amafutha glucocorticoid (wamafutha "boron-naftalan" "methyluracyl" kanye nabanye), epitelioplasticheskie amalungiselelo.
Ngo eside, kodwa ukwelashwa ayizwakali ngokuhamba ukusetshenziswa kwezimali angiotroficheskih. Lo muthi "dobesilate calcium", "ksantinola nicotinate" nabanye.
Kwenzekani kumuntu onalesi sifo yalesi sifo?
Onalesi sifo incike uhlobo vasculitis nobukhali sifo. ekuhlonzweni nasekwelashweni ngokushesha kungaba ngokuphawulekayo isikhathi ekuphileni isiguli. Kubalulekile lokwenza ukuxilongwa nokuthuthukisa i elilungile ukwelashwa lwemithi. Kumele kahle ukukhetha imithi umthamo ukuze ligweme izinkinga ezingase zivele futhi side effects.
Kuyinto engenakwenzeka ukubikezela umphumela izifo ezifana vasculitis letindzala. Ukwelashwa cishe uyoba ukuqhubeka nokuphila. Ngokuvamile, lesi sifo singumbulali okungamahlalakhona, izinkathi exacerbation kulandele izikhathi lapho ukuthethelelwa. Izifo vasculitis ngokuvamile hhayi belashwa ngokuphelele. Man njalo ophoqelelwe ukuvakashela udokotela nokulawula izimpawu.
Similar articles
Trending Now