ImpiloIzifo nemibandela

Angiomyolipoma kwezinso: Ingabe kuyingozi empilweni, Ubangela, Izimpawu kanye Ukwelashwa

Kangakanani izinso angiomyolipoma, kungaba usongela ukuphila? Lesi simo kusho ukuhileleka sokugembula inqubo interlayer amafutha, imisipha kwezicubu, futhi epithelium kwezinso. Ngo isimila ingozi ngaphezulu ingamafutha.

Njengomthetho, angiomyolipoma abelwa nezinso. Lesi sifo kungathinta umuntu wanoma yimuphi yobudala, kodwa abantu abadala kuyinto evamile ngaphezulu. Ngu iqembu ingozi kuhlanganisa abantu abasukela eminyakeni engama-40 kuya ku-60. Kufanele kuqashelwe ukuthi izimo ngokuvamile ezilotshwe abesifazane. Kungokungathi sína kangakanani lesi sifo, futhi aqede angiomyolipoma kwezinso? Ukwelashwa futhi izingozi ezibangelwa sifo, uzobe achazwe kulo magazini. Lapho esifike ngesikhathi okuqalwe yokwelapha zokugula luqedwe ngokuphelele.

zinhlobo isifo

Angiomyolipoma - isimila ingozi e-izinso. Lesi sifo futhi ithole elinye igama - "hamartoma kwezinso". Neoplasm libhekwa njengoba mesenchymal pathologies ezithinta kwezicubu ezithambile.

ezimbili kulomcimbi izinhlobo isifo: ifomu oqabukelayo yesifo okuyinhloko kanye zofuzo.

Esimweni sokuqala, isimila kuthinta umzimba ngokwawo, ngaphandle ufuzo, futhi esimweni sesibili, nendima evelele udlalwa ngu ufuzo.

Kukhona isifo esiseceleni ngokuphelele Bourneville-Pringle, noma ukuqina kwamathishu tuberous. Uma uthi ukulimala kwezinso, kodwa futhi ukhomba ezinye izimpawu.

Uma isimila itholakala izinso kwesokunxele noma kwesokudla kutholakala ukuthi uphethwe yini lesion sohlangothi olulodwa. Uma angahlangani sitholakale kokubili izinso, odokotela bathi ngohlobo zamazwe amabili. ifomu unilateral eba-75% amacala.

Ngaphezu kwalokho angiomyolipoma kungaba ejwayelekile futhi atypical.

Ifomu ejwayelekile ye isigaxa ngokuya iqukethe kwemisipha izicubu, noma amafutha emzimbeni, okuyinto zokwelapha landile.

Lapho ifomu atypical kwezicubu adipose akuyona. Lokhu inkimbinkimbi ukwelashwa. Ngenxa okunamafutha izicubu isuswe kungaphazamiseki. Futhi leli fomu kunzima ukuxilonga. Kulokhu, ematfuba delineation zamanga izimila ingozi futhi izimila ebulalayo.

Yini abatelekile lesi sifo?

Ngokuvamile, lapho isifo enqubeni sokugembula abathintekayo kanye cortex cerebral izinso. Ukuvuvukala kusiza ukwakheka capsule, okuyinto ebiyelwe nyá inyama ephilile.

Yini igcwele isifo esinjengo angiomyolipoma kwezinso (ngakwesokunxele nezinso ngakwesokudla)? Kuyingozi ngoba ngezinye izikhathi yenzeka lwesigameko okhethekile. Lokhu kwenzeka ngo-parallel izici ezilimazayo, isb yokwelapha ngokungalungile ekhethiwe noma khona pathologies ezengeziwe izinso.

Neoplasm zingase ziqhume ngo bakhiphe elezinga eliphansi vena cava, -lymph zitholakala eduze noma perirenal ngendandatho. Kwezinye izimo, ziyizitsha ethintekile negazi, okungase wavele nokuvuselela okuvela ukopha.

Abantu abaningi bayazibuza ukuthi yini angiomyolipoma esiyingozi? Ngokuvamile kutholakala ukuthi uphethwe yini kinking semithambo. Ngakho kukhona waphuka Kuvunguza okungase kubangele okukhulu ukopha zangaphakathi, ethwele usongo ekuphileni isiguli. Igazi lingena ngaphakathi komgodi ongaphakathi kwamathumbu futhi bevalela ke. izindonga Umhlinzi, aqukethe kwemisipha izicubu iba uqweqwe round, njengoba kwemisipha izicubu is ngokuphelele noma ingxenye siguqulelwa elihlangana. Umphumela kwasho perforation, lazo ezithusayo useshonile kanye nezinye izinkinga eziyingozi.

Izimbangela zesifo

Ukuthuthukiswa lesi sifo kungadalwa izizathu ezingafani nhlobo.

Ukuze zibe ziningana izici ayeke ukunisa kungase kubhekwe:

  • Ukukhulelwa. Ukubukeka isimila kuncike amazinga ama-hormone. Njengoba sazi, abesifazane ngesikhathi sokukhulelwa kwandisa izinga estrogen futhi progesterone, elingasebenza njengesibuko negalelo sokuthuthukiswa sifo.
  • Ngesisekelo zofuzo. Njengoba kushiwo ngenhla, lokhu kwakuphambene nemvelo kungavuka khona Bourneville isifo - Pringle. Lesisifo zofuzo. Ososayensi baye bathola ukuthi izakhi zofuzo kungenziwa ngofuzo.
  • A ezihlukahlukene isifo icubungula e ezinsweni, lapho okwenzeka kanye nezinye izinto, bangase avuse kahle isimila. Ukwelashwa, kulesi simo kuhilela ukuba kususwe yonke izifo eyayihambisana nalo.
  • Ukubonakaliswa nezinye neoplasms. Ngokwesibonelo, angiofibroma eba. Lokhu zokugula kuvamile. Kuchazwe isifo isihloko sika ucala kutfutfukisa ushukunyiswa yiwo.

symptomatology

ububonisa kanjani ngokwayo angiomyolipoma kwezinso? Eyingozi kakhulu lesi sifo? Nge ukwelashwa esifike ngesikhathi lesi sifo kungaba kwenziwe iqedwe ngokuphelele. Kodwa lesi sifo ngobuqili itholakala lokuthi ukuthi umlingisi abagqoka bakhathale ngasekuqaleni izigaba izimpawu. Izenzo sobala ngesikhathi isimila ehlasela.

Kwaphela izimpawu kufanele kubhekwe:

  • Siba nomuzwa ukusinda izinso kwesokunxele noma kwesokudla, kanye ngemuva. Ukungakhululeki kungenzeka esiswini bese wehlise emuva. Ubuhlungu kungenzeka edonsa, ezidabukile noma angenamusa. Basuke izimpawu a ukuqinaqina ngesikhathi ematfuba kanye nezinye izinhlangano zenkululeko. Lokhu kungenxa nokopha wendawo.
  • Jumps wegazi. Abakwazi zenzeka ngaphandle kwesizathu futhi ngokuvamile lokho kwanele.
  • Admixture wegazi umchamo.

Uma isimila uthola usayizi yisixuku, umculo ungakhuthaza itholwe palpation.

Imiphumela sifo

Uma imishanguzo kwenziwe ngendlela esifike ngesikhathi, kungase kube nemiphumela esongela ukuphila kwesiguli. Ngowokuqala ephule izitsha khona ukopha kungenzeka peritonitis. Nge ukopha ebanzi lapho esiswini kukhona osongweni lokufa.

Yini igcwele angiomyolipoma kwezinso? Kungakhathaliseki ukuthi ukuphila kusengozini uma ezuza usayizi esikhulu? Kulokhu, isimila bungasicindezela izitho eduze, ekuvimbeleni ukusebenza yabo ngokugcwele. Isibonelo, nge ukunqotshwa izinso esifanele isithasiselo onomfutho, ngisho isibindi. Neoplasm kungase ukudabuka, nakho uyingozi ekuphileni.

Enye inkinga enkulu wukuthola necrosis noma liyafa. Kulokhu, izinso umane ziyeke ukusebenza.

Ungakhohlwa ukuthi unesimila ingozi kungaba zibe isimila esibulalayo.

ukuhlola

angiomyolipoma kwezinso (izimbangela, izimpawu, zokwelapha ezichazwe kulesi sihloko) kudingeka uphethwe ngesikhathi esifanele. Ukuze ukwelashwa okuphumelelayo kumele kwenziwe ucwaningo abanekhono.

Eyokuqala Kunconywa kokuxilongwa ultrasound, ozokusiza ukuhlonza lwesimila. Kwezinye izimo, enifeza-magnetic resonance imaging kuyafaneleka.

izinga eliphakeme kahle ine jikelele ukuhlolwa kwegazi kanye nomchamo. Uyakwazi ukubonisa isimo uhlelo urinary.

Futhi, indlela biopsy isetshenziswa. Ukuze ngayo isimo yesimila izinso sithathwa kuhlaziywe nge ukuhlinzwa liquid noma wokubhoboza. Le ndlela yenza kube lula ukuxilonga khona umdlavuza.

Ukusetshenziswa kwezidakamizwa

Kukhona nobufakazi ukusebenza eliphezulu ezinye yizidakamizwa inhibitor leqembu. Ngemva kwalezi zifundo ezathatha, unyaka okuqhubekayo, kwezinye izimo, isimila kungancipha ngobukhulu ngesigamu.

Uma kukhona ukukhula ngokushesha kakhulu angiomyolipoma ke yakhetha indlela yokuhlinzwa.

Ngokuphathelene ukwelashwa abantu izindlela, ngokuvamile akukuniki neminye imiphumela.

izindlela zokusebenza

Ingabe izinso angiomyolipoma eziqhutshwa, noma ukuphila kusengozini uma kudingeka ahlinzwe? Kwezinye izimo, kuba usongo futhi kudinga ukususwa okusheshayo.

Ngokusekelwe imiphumela izindlela zokuxilonga akhiwa uchwepheshe yokwelapha uhlelo ngabanye, esidingeka acabangele izici ezibalulekile ezifana esigabeni lapho ukuthuthukiswa kwe-isimila, lingakanani kanye nendawo.

Ngokuhambisana namazinga zamanje emkhakheni of Oncology, isimila, ububanzi okuyinto mkhulu kunezinhliziyo 4 cm, siqedwa ngu uyephuza imiklamo. Le ndlela Kusekelwe ukuqapha ngezikhathi isimo lesiguli. Isiguli kuboniswa ubambe ultrasound kanye x-ray ukuxilongwa kanye ngonyaka.

usayizi isimila mkhulu kunezinhliziyo 4 cm zidinga ukwelashwa ezinkulu.

Ngaphandle kokweqa usayizi umbundu, inkomba ukuhlinzwa kuyinto:

  • uzwakalise isifo umtholampilo ukuba bathuthuke izimpawu umdlavuza;
  • ekwandeni okusheshayo yesimila;
  • khona ukwehluleka kwezinso, okuyinto kuba amahlala khona;
  • hematuria eyinsakavukela.

Ngo Oncology umkhuba for kuhlinzwa kokungenela kulindeleke ukusetshenziswa amathekhiniki alandelako:

  • Resection ingxenye ethile sezinso wamshaya isimila kungavamile ukuba ingozi. eyohlinzwa okunjalo uyakwazi ukugcina umzimba.
  • Embolization. Kule ndlela, umfula wangena apharathasi ekhethekile. Umthambo uyasondla aml. Izindlela ezinjalo neqhaza agqagqene inesikhala. Le nqubo ukhonza njengelungu esiteji wokulungiselela ngaphambi kokuhlinzwa. Ezimweni ezingavamile, embolization uba indlela ezimele yokwelashwa.
  • Enucleation. Phakathi ukusebenza, udokotela ohlinzayo kususa isimila ngaphandle umonakalo ezicutshini kwezinso komakhelwane.
  • Cryoablation. Kuyinto indlela innovative ukuqeda izimila yisithwathwa. Le ndlela yokwelashwa lisetshenziselwa esiningi lwesimila.
  • Ingabe Ohulumeni Banalo Lonke nephrectomy esinqunyiwe. Nge esibalulekile yesimila udokotela ohlinzayo enquma ukususa ngokuphelele emzimbeni.
  • Laparoscopy. Le ndlela kuhilela ukuqaliswa eziningi punctures ezivumela ukungena ekamelweni futhi ezandleni zomzimba.

ukuba nombono ongafani ngeke

Ingabe angiomyolipoma esiyingozi? Izibikezelo futhi ungafi amazinga abe mkhuba omuhle. Isimila kungokwalabo esigabeni izimila benign ise capsule. Lokhu kuwachaza kahle umphumela omuhle yokuphathwa. In iziguli eziningi, ngemuva kokuhlinzwa kukhona umuntu alulame ngokugcwele.

isiphetho

Kangakanani angiomyolipoma kwezinso, kungaba ezisongela ukuphila, liye ezichazwe kulesi sihloko. Pathology eyenani izifo ezingathí sina, kodwa uchayeke yokwelapha. Lowo oyinhloko uwukwenza Ihlahlubo ofeza impatho efanele.

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