ImpiloIzifo nemibandela

Ubuchopho Microcephaly ezinganeni: izimpawu. Microcephaly - a ...

Microcephaly - ke isifo esiyingozi. It kubonakala ngesimo ukuthuthukiswa okungavamile zazisa ubuchopho, kusho ukuncipha oqondile ngobukhulu bayo. Ngenxa yalokho, uma ifisa ukuba nomntwana ukuxilongwa imingcele endaweni ingqondo ngendlela ephambene neyemvelo encane kangaka.

zokugula incazelo

Microcephaly - isifo elinesimo ukwehla isisindo ubuchopho, lapho ukwehla kwemigomo kogebhezi ngqo selilonke ikhanda. Zonke ezinye izidumbu ziye ekuthuthukiseni ngokufanele wamukele ubudala kwezinkambiso. Izinguquko ezinjalo imbangela retardation engqondo futhi kwezinso ezingeni zezinzwa.

Ngokusho izibalo ezitholakalayo, lesi sifo sitholakale umuntu ingane 10000. Ukuba nobuhlobo ecacile emkhatsini phansi kanye ukubukeka ingane microcephaly sezihlonziwe.

Ebuchosheni, nale zokugula, zikhona izimpawu kombungu sina: Agnese Corpus callosum, heterotopia, Lissencephaly. convolutions cerebral imibono ezahlukahlukene isicaba, anemifantu ephakeme cishe lingekho ngokuphelele. Njengomthetho, izingane kwathiwa unesifo yesikhashana futhi frontal iyizingxenye, cerebellum, brainstem futhi thalamus ahlale ampofu.

Odokotela baye bathola izinhlobo ezimbili izifo ezifana microcephaly. Izimpawu ngamunye wabo basuke kucishe, kodwa avele ngezikhathi ezehlukene.

Ziyini izimbangela eziyinhloko zalokhu lesi sifo

  • Ukudakwa umbungu ngaphakathi esibelethweni ngenxa yethonya utshwala, izidakamizwa nogwayi, ngubani bayahlukunyezwa unina senyanga yokuqala sokukhulelwa.
  • Endocrine imvelo omama abakhulelwe.
  • Kudluliselwe lady abakhulelwe izifo ezithathelwanayo (isib toxoplasmosis).
  • Intrauterine ukutheleleka izinyane (mumps, isimungumungwana ne-rubella, i-herpes).
  • Ithonya amaqembu athile izidakamizwa.
  • umonakalo Mechanical noma ukulimala kwengane ngesikhathi sokubeletha.

Kaningi (34%) zobuchopho kubangelwa microcephaly chromosomal ukuguquka kwezakhi zofuzo. Ahlanganisa inqubo ekushintsheni isethi isakhi sofuzo, elibangela ukuthuthukiswa okungavamile ingane esibelethweni.

Kukhona amacala lapho abazali bezingane enempilo zizalwa ezinye ngeziphambeko. Nokho, sizazi sona ochwepheshe abakwazi ukuhlonza ngezici ezathonya ukuthuthukiswa lesi sifo.

emitholampilo isithombe

Ngaphandle lula microcephaly ukufunda, ikakhulukazi isifo kutholakala izingane ezindala. Ekuthuthukisweni evamile, ubuso izingane ogulayo imakwe hypoplasia zobuchopho ekhanda. Njengoba zikhula ziba izimpawu okubonakalayo isifo. ubuso womntwana ezinkulu, ebunzini olwehlelayo ihlukile, Nokho, ikhanda, uhlala encane.

Microcephaly ezinganeni kuzibonakalisa phezu kwekhanda ezincane kuya onyakeni, zazo selilonke lingaphansi kuka-34 cm. Nokho, lokhu isici akusona ezinkulu uphethwe wokugcina. Isikhathi esining impela, inhloko enkulu ngayo lapho usana - kuyinto isici ngabanye, ngofuzo njengefa kusukela izihlobo.

Kunenye ipharamitha ukuthi kungaba esibhedlela ukuhlonza isifo - esifubeni selilonke. Nale uphethwe, lesi sibalo kosayizi zekhanda selilonke, ngesikhathi izingane enempilo nxazonke.

Ngakho, odokotela ukuhlukanisa izibonakaliso elandelayo isifo:

  • Shona selilonke - 24-30 cm.
  • Rodnichok ivaliwe ngokugcwele usayizi encane noma ehlukile.
  • Kid ebunzini ewumngcingo, izindlebe ophumile kakhulu, ovelele brow lamagquma.
  • dystonia kwemisipha.
  • ikhanda ongalingani (ubuchopho amancane engavamile).
  • Ukuphakama nesisindo ingane ingaphansi kakhulu kunokuvamile.
  • Ngibanjwe.
  • Incoordination.
  • Strabismus.

Microcephaly - iyisifo lapho iziguli kancane ukucasuka esheshayo noma, kunalokho, njalo evilaphayo kanye ucobekile. Ziyakwazi isiqalo kuqhathaniswa ngasekupheleni ukugcina ikhanda lakho, uhlale ngisho ukukhasa. Ubuchopho izingane ezahlukene imikhuba eminingi emibi ngaphambili, isisindo sawo ingeqi uphawu 500 amagremu.

Kuye ngezinga of ukuncishiswa isifo ubuchopho wabonakaliswa degree ehlukene retardation engqondo. Esimweni ngasinye, sonke ngabanye. Ingane ingase unesifo degree sibi imbecility noma idiocy ifomu ngokujulile.

microcephaly azalwa naso

Ifomu eyinhloko lesi sifo ngokungavamile skull encane futhi ungakufanelekeli lokhu kobuchopho. Pathology kwakheka senyanga yokuqala noma yesibili yokukhulelwa ngenxa izifo ezibangelwa ufuzo noma isenzo yezici enqabayo kuchaziwe ngenhla. Izingane nale Ihlahlubo ithuba ukuqhuba ukuphila ezimele kwezenhlalo.

microcephaly yesibili

Izimpawu avame ephelezelwa i-cerebral palsy. Kwenzeka ngenxa yezizathu ongathandeki yokuthathu yesithathu yokukhulelwa, kanye ngenxa yokulimala kanye umonakalo mechanical ngesikhathi sokubeletha. izici okunjalo kungahlanganisa ukuhlukunyezwa unina utshwala nezidakamizwa. Iziguli ngaphezu yokuntuleka isisindo ubuchopho waphawula izinqubo ukuvuvukala, ukopha amaningi, izicubu necrosis. Ngesikhathi sokuzalwa sengane nekhanda ka- ingancishiswa kakhulu. Nokho, njengoba kubambezela ukuthuthukiswa kokukhula, ugebhezi iba ukuma azilingani, zikhona izimpawu retardation engqondo. Izingane abaye ukuxilongwa ukuqinisekisile of "microcephaly" kuleli fomu, ngokuvamile asikwazi ukuhamba noma ngisho ukuhlala siqonde.

ukuhlola

ukuhlola kwangaphambi kokubeletha kuhlanganisa ultrasound. Ngesikhathi inqubo, udokotela collates phakathi idatha ultrasound ubukhulu ikhanda fetus nomzimba nge izinyathelo zokulawula. Ulwazi Esinokwethenjelwa ingatholakala kuphela uma uma wazi kahle sokukhulelwa.

ukuhlola koda - yencazelo yokwanda koshintsho zezakhi zofuzo futhi kuma-chromosome. Ukutadisha okunjalo uqhutshwa ngesikhathi wokubhoboza of ulwelwesi bubble, njengoba indaba for cwaningo kukhona villi umbungu, kwi-amniotic fluid kanye izinhlayiya we epithelium.

Ukuhlolwa kumuntu okhulelwe kuhlanganisa ultrasound futhi igazi kwamakhemikhali. Futhi, isiguli bayacela ukugcwalisa ifomu lwemibuzo ekhethekile, okuyinto phakathi kwezinye izindaba, kukhona ikholomu yokukhulelwa. Idatha futhi imiphumela cwaningo okwenziwa uhlelo lwe-computer ekhethekile elikhombisa amathuba izifo ezifana ingqondo microcephaly.

Ukuhlolwa Newborn Kwenziwa ngemaminithi ekucala nje emva kokuzalwa ngesisekelo imingcele ezibukwayo. Uma uphethwe kuqinisekisiwe, ukuhlolisisa esibanzi uqokwa kamuva.

Yini okufanele baphathwe?

Microcephaly - kuhle kwesifo esingelapheki esidluliselwa, ukubuyisela umsebenzi evamile ubuchopho akunakwenzeka, kodwa kunezindlela yokuyala yayo.

isifo Ukwelashwa kuhilela indlela olunzulu, imisebenzi ezivame okuhloswe ngazo ukuthuthukisa nokuhlakanipha kwengane ukuze lithathelwe walo omkhulu emphakathini.

Ukwelashwa yenzeka ngezindlela ezintathu:

  1. ukwelashwa. Isetshenziswa ukuze sikhuthaze izinqubo umzimba kwenza ubuchopho. Ngenxa yale njongo, esimisiwe sedatives, anticonvulsants olubi nokuphela kwamanzi emzimbeni ( "Nootropil", "piriditol" "Cere").
  2. Physiotherapy, umsebenzi yokwelapha, ukubhucungwa.
  3. izinyathelo zokwelapha ukulungisa kwengane bokusungula. Ezweni lethu kukhona izikole ezikhethekile boarding izingane sezinzwa uhlelo izilonda, kanye sitholakele "microcephaly". Izithombe izingane ezihilelekile izinhlangano ezinjalo, kungatholakala kulesi sihloko.

Ukwelapha seziguli ezisencane ne eyinhloko lesi sifo ngezinye izikhathi kuphumelele. Lapho abakhethiwe kahle ukwelashwa kasoze Impilo ephelele, kodwa ngeke akwazi ukuqhuba ukuphila okulula nomphakathi.

Njengoba for ifomu lesibili, lapha izinto zimbi kakhulu. Izingane eziningi, naphezu ukwelashwa sina nokuphikelelayo, awukwazi ifa amakhono aphansi kakhulu.

ukuba nombono ongafani ngeke

Microcephaly - a zokugula, elibangela thuthuva ingqondo okungathí sina. imithi yesimanje, ngeshwa, ayinikeli projection esiduduzayo maqondana iziguli unesifo. Qedela ikhambi akunakwenzeka. Umsebenzi oyinhloko odokotela nabazali ukufundisa ingane kuyintfo lesembili amakhono self-service, lokuthi babuyisele umsebenzi evamile motor.

Ngokusho izibalo ezitholakalayo, isilinganiso sobude bokuphila kwabantu nge microcephaly ngenxa yokuntuleka ukuthuthukiswa futhi ukusebenza kwengqondo kuyinto iminyaka 12-15. Kakhulu akuvamile, abantu baphile iminyaka engu-30. Ngokuvamile, abantu nalesi sifo ngingofayo kusukela izilonda zaso.

zokuvimbela

ubuchopho microcephaly - isimo iyivelakancane ukuxwayisa ukuthi akunakwenzeka ukuthuthukisa. Uma umndeni isivele ozalwa ingane nale hlobo anomaly, ochwepheshe batusa abazali ukuba baphumelele ukuhlolwa kwezokwelapha kanye zofuzo ezikhethekile ukuhlola ingozi isifo esifanayo kulezi izingane.

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