Proteus Syndrome: Izimpawu kanye Ukwelashwa Izindlela

Kuze kube manje, Proteus syndrome kuthathwa njengesibikezelo ezingavamile kakhulu isifo esidluliselwa ngofuzo, okuyinto kuhambisana ukukhula okungesona esingokwemvelo amathambo, imisipha nezicubu zezinzwa. Ngeshwa, ukuxilongwa kanye nokwelashwa kwezifo ezifana - nenqubo enzima kakhulu futhi ngaso sonke isikhathi kungenzeka.

imithi yesimanje, kuphela Proteus syndrome kuyisifo esiwufuzo futhi lihlotshaniswa kuguquka zezakhi zofuzo kwaziwa. Nokho, lo mshini ukuze nesenzakalo yalezi zinguquko is akukaqondwa ngokugcwele.

Proteus Syndrome: Umlando kancane

Ngokokuqala ngqá leso sifo achazwa 1979. Kulapho Maykl Koen okutholakele mayelana 200 amacala yilesi sifo emhlabeni wonke. Kwaba lesi sazi futhi wanika igama sifo. Proteus - ulwandle unkulunkulu e zamaGreki. Futhi, ngokuvumelana izinganekwane basendulo babengazi, lokhu unkulunkulu angashintsha ukuma nosayizi komzimba wakhe.

Proteus Syndrome: Izimpawu

Empeleni, lesi sifo kungase kuhambisane ezihlukahlukene izinguquko neziyaluyalu. Njengomthetho, izingane ezigulayo bazalwa ngokuphelele evamile, futhi kuphela iminyaka yezinguquko uqale. Ngokuthakazelisayo, esimweni ngasinye, izimpawu zingase zihluke. Kwezinye iziguli, a kofuzo kunqunywa ithuba, ngoba akukho izimpawu zangaphandle ungekho. Abanye iziguli, kunalokho, cishe konke ukuphila kwakhe abaphethwe kabi.

Njengoba sekushiwo, Proteus syndrome (esesithombeni) ephelezelwa ukukhula kwezicubu - kungaba imisipha, amathambo, isikhumba, izindlala futhi imithambo yegazi, okunamafutha izicubu. Neziqu ingavela cishe noma kuphi. Ngokwesibonelo, kukhona ngokuvamile ukwenyuka ubukhulu ikhanda, izingalo nemilenze, ushintsho ifomu yabo evamile.

Kufanele kuqashelwe ukuthi isilinganiso sobude bokuphila kwabantu sinciphile. Ziyakwazi bathambekele kakhudlwana kunabanye yezinkinga isimiso sokujikeleza kwegazi (embolism, deep vein thrombosis), kanye umdlavuza futhi goiter.

Ngu uqobo, Proteus syndrome akakubangeli ukubambezeleka zentuthuko. Kodwa ngenxa overgrowth kakhulu izicubu kungenzeka izilonda yesibili isimiso sezinzwa.

Proteus Syndrome kanye nokwelashwa kwayo

Okokuqala-ke Kuyaphawuleka ukuthi ekuhlonzweni kubaluleke kakhulu. I ngaphambili lesi sifo uchazwa, iyoba sethubeni elihle lokuba ingane ukuphila okunethezekile. Njengazo zonke izifo zenani elikhulu eziyifa kanye azalwa naso, inkinga akusona isixazululo esisodwa - akunakwenzeka ukuqeda lesi sifo. Kodwa izindlela wokuphila emkhakheni wamuva wezokwelapha kuzosiza ukulwa izimpawu eziyinhloko.

Ngokwesibonelo, lapho ukukhula ithambo izicubu, ukugobeka komhlandla, ubude ezahlukene nemilenze mhlawumbe egqoke amadivayisi ezikhethekile wamathambo ukusiza ukubhekana kangcono nale nkinga. Uma lesi sifo lihlotshaniswa kwezinso ku isimiso sokujikeleza kwegazi noma isimila, isiguli kufanele ahlale ngaphansi ebhekiwe zikadokotela.

Kaningi esetshenziswa futhi ukwelashwa kuhlinzwa. Ngokwesibonelo, usebenzisa ukusebenza ungalungisa yizinyoka, mfushane amathambo neminwe, ukuthi umuntu angasebenzisa ngezandla zombili. Ngezinye izikhathi kudingeka ulungise amathambo ezicutshini of the thorax, ukuze akhulule nesineke kusukela ezinkingeni singagwinyi.

Kunoma yikuphi, lokhu isifo kudinga ukunakekelwa njalo futhi ukunakekelwa. Okuwukuphela kwendlela yokuthola ukuphila futhi ekuthuthukiseni izinga layo.