Impilo, Izifo nemibandela
Lefgrena syndrome: Izimbangela, izici yomtholampilo, ukwelashwa, zokuvimbela
izifo lefundo bezilokhu imfihlakalo emhlabeni wezokwelapha. Esinye sazo sarcoidosis, eye kungafaneleki etiology futhi eboniswe ngendlela ukuvuvukala ezicutshini kwezitho zomzimba ahlukahlukene nezicubu kumiswa granulomas. Lefgrena syndrome - a okhethekile sarcoidosis ezithinta esikhumbeni, intrasternal lymph node kanye namalunga.
izimbangela
I pathogenesis ukuthuthukiswa impendulo sokuhlasela kwamasosha omzimba. Amasosha omzimba ukuphahlazeka, futhi amangqamuzana amhlophe egazi uqale hit enempilo wamaphaphu amaseli, amalunga isikhumba.
Lefgrena syndrome ngokuvamile eba abesifazane abasebasha (iminyaka 20-35). Izingane ngokuvamile abazi agule. Lefgrena syndrome uqala babazi, bese kancane kancane izenzo zokwelapha kungase ngokwabo zenzeke. Ngokuvamile, kukhona Yiqiniso evumayo lesi sifo.
Ngaphandle theory ezibangelwa amagciwane kanye ezibangelwa amagciwane yentuthuko sarcoidosis, kukhona inkolelo yokuthi lesi sifo eba abantu isikhathi eside nabo amakhemikhali oluyingozi ezimbonini. Akufanele sikhohlwe, kanye isici sitholwa njengefa. Yingakho sarcoidosis polyetiological kuyinto isifo sokuhlasela kwamasosha omzimba.
ukubonakaliswa emitholampilo
Lefgrena sifo ngo sarcoidosis ububonisa polisimptomno. ukubonakaliswa Clinical uqale babazi. Umuntu has erythema nodosum emzimbeni, it has ukuthambekela ukusakaza emikhawulweni, emuva, isisu nentamo. ISIZINDA une-kobujamo obusaqanda, ubukhulu babo bangase afinyelela 6 ngamasentimitha. Kufanele kuqashelwe ukuthi esikhundleni kumiswa erythema ingekho necrosis.
Ukubonakaliswa main kubhekwa ukuba kokunqotshwa bronchial kanye tracheal nezindlala. Lokhu kukhomba ingozi enkulu ukuze isiguli:
- ukukhwehlela;
- ngezikhathi ezithile kukhuphuke izinga lokushisa komzimba;
- ukuwohloka kwempilo;
- kukhona ukujuluka ebusuku;
- eziwohlokayo nobuthongo;
- kwesisindo kwenzeka;
- umuntu ahlangabezane ukukhathazeka.
Kamuva Lefgrena syndrome libhekene izilonda amalunga omzimba. Njengoba eqhubeka ehamba aba buhlungu edematous futhi ukuhamba liwohloka. Ngomqondo ovulekile, omunye ungaphawula ukuvuvukala-lymph entanyeni e emakhwapheni.
Indlela ukuxilonga?
Lefgrena syndrome Kumiswa ngesisekelo ukuhlola laboratory kanye Ukuhlola owelapha lesiguli. Erythema nodosum udlala ezibalulekile ekuhlonzweni lolu hlobo sarcoidosis. Nokho, lo dokotela kumele ahlukaniswe kusuka isifo sofuba noma izifo dermatovenereological.
ukuhlolwa kwegazi Laboratory sizobonisa:
- anda ESR;
- leukocytosis;
- ukubukeka ye-gamma globulin.
Ku-X-ray isithombe kungabonwa isici lakhulisiwe zamanzi, kanye ezifakwa fibrous. Lokhu kusiza ukuba uqiniseke esimweni isifo samaphaphu.
Wavuma obonakaliswe ifomu kudinga bronchoscopy nge biopsy. Lapho ekutadisheni wamaphaphu izicubu abakwazi ukubona izici isakhiwo histological ka sarcoidosis: uzingela izakhi granulomas epithelioid.
Izibikezelo kanye nezinkinga lesi sifo
Ngamunye ageleza Lefgrena syndrome. isikhathi esingakanani futhi yiziphi izibikezelo kungase ukuphendula kuphela izimfuneko ezithile. It is ukuthi amadala umuntu, onalesi sifo esibi ezaziwayo. Uma azisebenzi ngesikhathi ukuze ubone udokotela, lesi sifo imisiwe futhi ejoyinile ngu yezinkinga:
- isimiso bronchial;
- esingamahlalakhona zokuphefumula;
- ukuthuthukiswa "inhliziyo yamaphaphu";
- emphysema;
- a flora virus.
ukuhluleka zokuphefumula eba ngemva isimiso bronchial. isimo wesiguli kancane kancane eziwohlokayo njengoba amaphaphu ziqala ukuba kubekwe ezicutshini, inqubo zingayeka angesabi emva kweminyaka 1-2.
Kancane kancane, inhliziyo uqala ukwandisa ngenxa yokushodelwa umoya egazini. Kodwa akufanele indiva isikhalazo bathole usizo lwezempilo, ngoba manje Lefgrena syndrome esilaphekayo.
ukwelashwa
Ngeshwa, Medco ayikwazi ukwelapha ngokuphelele sarcoidosis, kusukela omsakazo yayo akwaziwa ngokuphelele. Kodwa odokotela linqume ukwelashwa ekhethekile uyakwazi ukumisa inqubo ukuthuthukiswa, ukuqapha Lefgrena syndrome. Ukwelashwa iqala lapho uya khona steroidal izidakamizwa eqeda ukuvuvukala ngoba amasosha omzimba aphansi. Futhi ebekiwe Vitamin izakhiwo, Antioxidants, immunosuppressants.
Inkambo yokwelashwa ihlala okuyisilinganiso sabangu-izinyanga 8. Konke kuncike izici ngamunye kwesimiso somzimba sokuzivikela ezifweni. Advocates saziso wezokwelapha isheke-up abagulayo udokotela pulmunologom, kungakuhle kakhulu-ke ihlala iminyaka engu-5.
Uyini zokuvimbela?
Ukuvimbela ukuthuthukiswa sarcoidosis, kufanele kuqala eyoqaphela indlela yabo yokuphila. Ukudla kufanele balinganisele, zimumethe amafutha, amaphrotheni, carbohydrate i isilinganiso elikhulu.
Abantu beyizidlova sarcoidosis, kufanele ukuyeka ukubhema, ukuxhumana nolaka ikhemikhali.
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