Impilo, Imithi
Cerebellar hypoplasia: Izimbangela, Izimpawu kanye Ukwelashwa
Akekho ogonyiwe kusukela okuvela yisiphi isifo. Kodwa kwezinye izimo sifo ucala kutfutfukisa esibelethweni kanye ingane ngesikhathi sokuzalwa wembula zokugula ezahlukene. Omunye isifo ezinjalo kuba hypoplasia cerebellar - isifo esithinta ingqondo yengane.
incazelo
Cerebellum - ingxenye yobuchopho, okuyinto esifundeni ezingemuva futhi ebalulekile isimiso sezinzwa esiyinhloko. Lokhu umzimba obangela kokuxhumana ukunyakaza, imisipha iphimbo, ikhono ukulinganisela kwakhe. Cerebellar Hypoplasia isihlava ephelezelwa ukwehla ngendlela eyodwa noma ezimbili yezingxenye zayo.
izizathu
hypoplasia Cerebellar ku omdala - phetho okungafanele kwengane esiswini, kanye izimbangela yalesi sifo kuthiwa egxilile endleleni yokuphila yowesifazane okhulelwe. Kunezici eziningana ezinkulu engabangela ukuba isifo.
- Ukusetshenziswa kotshwala.
I eziyingozi kakhulu ukwakheka utshwala kuyinto ethanol. ephuza ke lingena fetus isimiso sezinzwa esiyinhloko, ukuze kuvuswe kumiswa izinhlobo ezahlukene izimila. Futhi, i-ethanol kuyinto enamandla okubhubhisa isithiyo yemvelo evikela ezifeni we CNS, engena phakathi umzimba ngemithambo yegazi. Ngokuvamile, ukuhlukunyezwa utshwala ngesikhathi ekhulelwe udalula impilo i-fetus engozini enkulu.
- Ukubhema.
Ngokuphambene nalokho okukholelwa yiningi nomthelela ongemuhle i-fetus iyakwazi kungekho nicotine kanye nezinye ezinobuthi ezakha usikilidi. Zingadala malformation neural tube, futhi kungakho ubuchopho fetus nomgogodla. Lapho ngokubhema ngesikhathi sokukhulelwa hypoplasia cerebellar eqoshiwe njalo.
- Ukusetshenziswa kwezidakamizwa.
Izidakamizwa kungathinta isimiso sezinzwa njengoba okhulelweyo, ingane, ngakho ukusetshenziswa yabo akuvumelekile kuzo zonke izimo. Izinto ezinjalo idale umonakalo ongalungiseki umzimba okwagcina siholela ekufeni.
- Reception izidakamizwa ezinamandla.
izidakamizwa abaningi banqatshelwe ukusetshenziswa ngesikhathi sokukhulelwa. Indlela yabo inikezwa kuphela uma isidingo esikhulu. Ngokumelene okwenza yokwelapha yezokwelapha nolaka angagcina hypoplasia we cerebellum ku-fetus.
- Ukuchayeka emisebeni.
isotopes Radioactive bathambekele buthelela kwi-amniotic fluid kanye umzanyana, kungaholela ukuguquka kwezakhi zofuzo-DNA ingane. Ngemisebe noma ubude ukuhlala ezindaweni amazinga high emisebeni igcwele yezinkinga eziyingozi ngoba umama okhulelwe kanye nengane.
- Izifo ezithathelwanayo.
hypoplasia Cerebellar kungenzeka kwenzeka ukuthi owesifazane okhulelwe kuzothatha lesi sifo obonakala ulula njenge nesimungumungwana. Empeleni, lesi sifo yegciwane kuyingozi kakhulu. Lapho ukutheleleka senyanga yokuqala, odokotela abaningi batusa sokuqeda ukukhulelwa, njengoba ingozi kwezinso ku-fetus kuphezulu kakhulu. Ngezinye izigaba kamuva ababa nakho abesifazane imithi inikezwa, kodwa uphumelele kuphela 50% amacala.
Iphinde ibe yingozi mkhulu toxoplasmosis, okungase wacosha uma nabo amakati ogulayo, namagundane nezinyoni. Lokhu sifo hhayi nje nomthelela ongemuhle kwengane esiswini, kodwa zonke kungabangela ukuchitheka kwesisu.
Ngaphezu zonke izizathu ngenhla, udinga eceleni yisho ukudla ezilimazayo, lihambisana nezinye izinto zaba nomphumela kungathinta Yiqiniso yokukhulelwa.
izimpawu
Hypoplasia we vermis cerebellar wengane kuhambisana ukuhlukumeza imisebenzi eminingi ngesimo somzimba. Ochwepheshe ukukhomba zimpawu ezilandelayo:
- eliqhaqhazelayo (ukuthuthumela) ikhanda, engenhla futhi emikhawulweni aphansi;
- ukukhuluma ngokhahlo, okungukuthi, ingane ukukhuluma okuningi okufana yelping;
- ukunyakaza izinyane ulahlekelwe olubushelelezi zabo futhi babe abathathela;
- izingane hypoplasia cerebellar ukuthuthukisa kancane kakhulu, okungukuthi, ahlale, ukukhamba nokukhuluma beqala umhla ontanga yabo;
- imisipha isiqu nasemilenzeni uncoordinated encishisiwe - ngenxa yalokhu, sukuma noma ahlale phansi ingane iba nzima nakakhulu;
- izingane ezinjalo kuba nzima kakhulu ukugcina ukulinganisela, kokubili ukuma isikhundla ihlezi;
- ukunyakaza ngaphandle nezinsiza cishe akunakwenzeka, kodwa uma abantu usazokwazi ukufunda ukuhamba, Gait bakhe kuyinto angahleliwe kakhulu;
- futhi kukhona ukuphazamiseka bemisipha abushelelezi viscera;
- abantu hypoplasia cerebellar ngokuvamile baphazamisekile imisebenzi zokuphefumula;
- izingane osanda kuzalwa ngokumelene isizinda sifo sivame ukuba khona ubuthulu noma ukuba yimpumputhe.
Isibonakaliso osobala kakhulu hypoplasia cerebellar e ingane - wezimbangi, Gait zithonye futhi kuphula umthetho we orientation ngekwendzawo. Futhi, abantwana bakwa-ubukhulu skull lincane kakhulu kunokujwayelekile, ngoba ubuchopho babe ngaphansi kuka banezingane eziphile kahle. Njengoba ikhula usayizi Yiqiniso, ukwanda, kodwa ukusonteka ikhanda kwangathi zisekhona.
hypoplasia Cerebellar iqhubeka Eminyakeni yokuqala 10 yokuphila kwengane, ngemva kwalokho isimo sakhe uhlaliseke njalo odokotela linqume ukwelashwa esekelayo.
ukuhlola
Ngokuvamile, isifo itholwa ngesikhathi sokukhulelwa by odlula ultrasound ukuhlola. Okwalandela ingane observation obonisa wezinzwa. Angaba linqume ukwelashwa noma nokuvuselelwa nezinqubo.
ukwelashwa
Ngeshwa, hypoplasia cerebellar kubhekwa isifo esingalapheki, futhi abantwana abakhula ngaphansi sizalwa ke, kuyaqabukela ukuphila ngokuvumelana ngonyaka. Zonke izinqubo abazenzi nengane, okuhloswe ngaso ekubuyiseleni imisebenzi elahlekile futhi containment lesi sifo. Izinqubo ze-zokwelapha zihlanganisa:
- umzimba okuhloswe ngazo ukuthuthukisa ukuxhumana;
- massage;
- ukulondoloza amakilasi inkulumo nodokotela osiza abanezinkinga zokukhuluma, udokotela;
- futhi nezingane kunconywa kaningi ngangokunokwenzeka ukuxhumana sifake kuzo ezihlukahlukene izinto zokuchitha isizungu, ezifana imidwebo noma origami ukuthi ukuthuthukisa amahle motor finger.
zokuvimbela
Ukuvimbela lesi sifo ngendlela enempilo of kokuphila kukanina esizayo. Phakathi nenkathi yokukhulelwa, udinga athintane nodokotela ngaphambi ukusetshenziswa kwanoma yiluphi izidakamizwa, futhi ususe ngokuphelele kusukela ukuphila utshwala yakho, ukubhema, izidakamizwa, nokunye. D.
Noma yimuphi isifo kulula ukuvimbela esingayenza ngaphandle kokuthi siphathe. Ngakho-ke, uma owesifazane kahle ukuzinakekela uthwele ingane, ingozi kwezinso is kakhulu ziyancipha.
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