Impilo, Izifo nemibandela
Ukukhubazeka Duchenne-ERB: Izimbangela Nezingozi Ukwelashwa
ukuthuthukiswa imithi njalo. Nsuku zonke, ososayensi usungula imithi emisha ukunikeza izindlela ngcono imisebenzi esiqhuba. Nangale kwenqubekela phambili enkulu kule ndawo, inkinga lokuzalwa ukulimala namanje efanele. Ingozi embi kunazo zonke uthela hhayi zokugula nemiphumela yaso. Isibonelo esiyinhloko yisifo esithinta izinzwa, okuyinto ingane angathola ngokuhamba ukulethwa, a brachial plexus ukulimala. Uma izinguquko ebonwe isakhiwo amathambo wesibeletho, ukukhubazeka ukuthi une-Duchenne-ERB. Ziyini izimbangela eziyinhloko zalokhu yesifo nezindlela zokwelashwa kuzoxoxwa ngezansi.
incazelo emfushane isifo
isifo neuropathy isimiso sezinzwa esakheka ngenxa ukulimala ebuchosheni brachial plexus libizwa Duchenne-ERB. Ivame kwandulelwe kokulimala lokuzalwa. Ngakho-ke, i-pathology uvame ukubizwa ngokuthi ukukhubazeka azoya. Nokho, lokhu akukhona imbangela kuphela kulesi simo.
It libhekene ukuba buthakathaka kwezicubu e emikhawulweni engenhla, izivimbelo ukuhamba ehlombe futhi indololwane amalunga omzimba. Libuye kungenzeka yini ukuthi kwephulwe ukuzwela, kodwa agcinwayo motility emabhulashini. Zokubelethisa Duchenne-ERB palsy sika kungenzeki ukuba banqobe, uma sisebenzisa uhlelo jikelele ukuze athole ukwelashwa. Ukwelashwa njalo kukhethwe ngamunye. Esinye isiguli esingumuntu emva, udokotela ekunika imithi eyanele, abanye - Physiotherapy. Ezimweni ezinzima kakhulu ezidinga ukuhlinzwa. Isibikezelo ukutakula incike ngobucayi zokugula futhi ukuphelela nokwelashwa kwayo.
Isizinda esingokomlando kanti ezinye izibalo
Ukukhubazeka Duchenne-ERB ukuthi ogama lakhe behlonipha neurologists ezimbili. Baqale ukuchaza ngokuningiliziwe etiology lesi sifo futhi emtholampilo. French udokotela G. Duchesne iminyaka eminingi ukutadisha isimo seziguli ezisencane ngemva kokuzalwa nzima. Ngo-1872, wafingqa Imininingwane wathola wasethula incazelo eningiliziwe izimpawu ukukhubazeka in izinsana. Parallel ekutadisheni sifo abathintekayo omunye udokotela evela eJalimane W. ERB. Wakwazi ukuchaza isithombe yokwakheka ukuthuthukiswa yesifo nayo pathogenesis yale nqubo kwabadala.
Ngokwezibalo, ukukhubazeka azoya ka-Duchenne-ERB iwela isigaba pathologies ezingavamile. Okwamanje, kokutshelwa ngokukhubazeka kwengane kuqinisekisiwe zonke osanda kuzalwa senkulungwane. Naphezu ngcono njalo amasu azoya, lesi sifo ihlala inkinga nezokusigcoba wokuphila emkhakheni wamuva wezokwelapha.
Izimbangela ukukhubazeka e izinsana
Ukukhubazeka Duchenne-ERB kule osanda kuzalwa eba ngaphansi kwesimo kuhlasimulise plexus brachial. Ngo inqubo kokubeletha, lesi obelethisayo has ukwenza izenzo ezehlukene ukusiza ukuba kokuzalwa komntwana. Kufanele kuqashelwe ukuthi wenziwa izinyathelo ezinjalo kuphela uma eziphuthumayo. Kulezi manipulations zingenzeka:
- ukuhlukumezeka imisipha isitebhisi ;
- esisuka we plexus brachial, emsipheni enqwabelanisa amakhefu;
- ukopha okuncane endaweni ethintekile.
Uma umbungu likhulu kakhulu, kanye nemingcele yayo awafani usayizi emgudwini wokuzala, ingozi ukulimala ehlombe inyuka ngokuhlanganyela izikhathi eziningana. Ukusiza wayeyozalelwaphi ingane yakho, ababelethisi bephoqeleka ukuba usebenzise amathuluzi akhethekile. Ngezinye ukunyakaza abukhali le brachial plexus yezinzwa amakhefu.
Izimbangela ukukhubazeka e abadala
Ngo izingane ezindadlana nabantu abadala, ukuthuthukiswa kwe-pathology kuvame ukuhlotshaniswa uhlukunyezwe. Phakathi kwalezi umonakalo mechanical zihlanganisa:
- traction ingalo;
- intamo ukulimala;
- brachial plexus ukulimala ezonini;
- ngilulekela.
Ngezinye izikhathi brachial plexus ukulimala kungenxa yakhe engozini yemoto. Akuvamile kakhulu ERB-Duchenne ukukhubazeka e abadala kuphakama kusukela lesion enobuthi noma ezithathelwanayo. Ukuthuthukiswa inqubo sokugembula kungadalwa soFuba ogeleza eziyinkimbinkimbi ifomu, imfiva, nomalaleveva.
Yiziphi izimpawu zibonisa isifo?
With ukuthuthukiswa okuthiwa ukukhubazeka flaccid waphawula ukulahlekelwa umsebenzi eziningana imisipha (izikhwepha, deltoid, ehlombe). Kobukhulu izimpawu umonakalo incike uhlobo endwangwini, ishayela conduction kwezinso.
izinsana palsy Duchenne-ERB sobala ezinsukwini zokuqala zokuphila Iningi. Ingane iba sikhathazeke ngokweqile futhi njalo ekhala. Imbangela sifo sebuhlungwini obunzima ezingalweni nasemilenzeni. Futhi phezu ukulimala brachial plexus kungase kubonise zimpawu ezilandelayo:
- njalo futhi kancane wavula isandla endololwaneni;
- kwehle imisipha ithoni;
- encishisiwe emoyeni;
- isandla isango isibhakela ne isithupha;
- isikhumba okhanyayo.
Nakuba engakwazanga ukuwaphendula womsebenzi esandleni obuhlungu, izingane ngokuvamile aba ongaphakeme traffic ivolumu. Nokho, uma nosana walala flat ku entendeni esitho ethintekile uzobe kancane droop.
Izigaba sokugembula inqubo ukugeleza
Ukukhubazeka Duchenne-ERB ithuthukiswe ngezigaba eziningana.
isigaba olunamandla Uthatha amahora ambalwa izinsuku 2-3. Ngalesi sikhathi, kukhona ukwehla yomsebenzi wezandla, ubunzima eguqa ingalo endololwaneni yenqubo.
Bese kufika esigabeni yokutakula. Ngokwelashwa okufanele we yokulungiswa imisebenzi elahlekile angase kuthathe iminyaka eminingana. Ngenxa yalokho, esikhathini ukulimala kwenzwa fibre le edema esenyamalala, ukuzungeza igazi esimweni sayo ngokuphelele.
Ngemva kwalokho eza esigabeni yemiphumela asalile ukuthi eziyohlala phakade. Ngakho-ke, kubalulekile ngesikhathi yokutakula imatasa ukwelashwa. Enkundleni, yimuphi imiphumela bokungasetshenziswa ezelaphayo lingama ayizwakali. Isiguli abathintekayo esitho kancane kancane hypertrophy, kuyilapho abanye balimale kanzima ubukeka abonisa ukungavuthwa. Ikhaba ngohlangothi isiguli nabokhulumile, onqenqemeni asuka emgogodleni. Ngokuhamba kwesikhathi, lezi zinguquko kuholele ugobile yomgogodla - ukugobeka komhlandla.
yikona kanjani?
Izibonelo Duchenne-ERB ucwaningo palsy namanje riveting ukunakwa ososayensi ezivela emhlabeni wonke. Nokho, namuhla uphethwe yenqubo sokugembula akubangi nobunzima. Lapho izimpawu zokuqala wezingane zakhe kufanele uthumele ezizalwayo babonisana ne isazi sezinzwa futhi wezifo zamathambo. In iziguli omdala, ukwelapha isifo zihilelekile kulo lezi ochwepheshe. Ukuze ukuxilongwa udokotela wezinzwa Kufanele itadishe umlando isiguli usingathe ukuhlolwa ngokomzimba. Khona-ke ukuthuthela ukuhlolisisa olunemininingwane ethe xaxa kuhlanganisa:
- electroneuromyography;
- MRI;
- ikhompyutha myelography;
- dinanometriyu;
- reovasography;
- Ultrasound ukuhlola joint ehlombe.
Ngokuvamile, ukubonakaliswa kwangaphandle isifo kwanele ukuqinisekisa sifo. Zonke ulwazi oludingekayo ukuze afakwe ikhadi wezempilo wesiguli. Udokotela wenza inothi, lokwenza ukuxilongwa, "ERB-Duchenne ukukhubazeka." ICD-10 anikezwe ikhodi isifo R14.0.
Nokho, ukuze abone ubunjalo umonakalo kokuqhuba lezi zifundo liyadingeka. Ngamunye izindlela ukuxilongwa ithwala umsebenzi othile futhi ayikwazi kuphenduke ngenye. Ngokusekelwe kulezi imiphumela yokuhlolwa, udokotela wakho angase akunikeze imithi yokwelashwa, kanye ukunikeza isibikezelo esizayo.
ukwelashwa
ukwelashwa ukukhubazeka iqala izindlela olandelanayo. Esigabeni acute akwenzeki ngaso sonke isikhathi ukunquma izinga lomonakalo kumafayibha ngenxa izicubu edema eqinile. Ngakho-ke, izinqubo kuhlinzwa abhekwa okungalungile.
Yini imithi asetshenziswa ekulweni le zokugula, elingenhla palsy Duchenne-ERB?
- izidakamizwa Nonsteroidal eqeda ukuvuvukala: "ibuprofen", "Amidopyrine".
- Imithi ukuthuthukisa kwegazi, "Pentoxifylline," "papaverine".
- izidakamizwa Anticholinesterase ezithuthukisa amaza kwenzwa "Neuromidin", "galantamine", "Neostigmine".
- Amalungiselelo ukuzinza lokugayeka kokudla "Aktovegin", "Meksidol" Vitamin izakhiwo.
Nge ngcono lesiguli imithi umthamo kanye umthamo lwemithi ziyahlukahluka.
izinqubo ukwelashwa ngokomzimba
Ukulwa inqubo isifo kusho okuthiwa isikhundla ukwelashwa. On esitho egulayo is esikhulu ibhasi ezingasetshenziswa zisuswe ngesikhathi nezinqubo inhlanzeko kuphela.
Ukuze silondoloze imisipha ithoni imibukiso, imisebenzi efana:
- uhlikihla esitho ethintekile (uqale kusukela evikini lesibili);
- kagesi imisipha ukushukuma ;
- Physiotherapy kanye nokuvivinya umzimba ngendlela nje kuphela;
- ukutshopa;
- upharafini zokugeza;
- ozokerite.
Umphumela omuhle yokwelapha olandelanayo kungenzeka kuphela uma ezicekeleké ka kwezintambo zesivikelo sesifuba brachial plexus. Wayelindele naye kungathi izinyanga ezintathu, bese uqhubekela phambili kokuhlaziywa kwemiphumela. Uma okwamanje isiguli ayibonakali ukunyakaza asebenzayo we indololwane, umbuzo mayelana nokusebenza.
kokungenela kuhlinzwa
Ingqikithi yalo msebenzi encishisiwe ukubuyisela ubuqotho imicu lilimele. Ngenxa yalesi ukuziphatha emsipheni isiqu plastic. Okwamanje kuba ukusebenza kuphela ezingakusiza iziguli kwathiwa unesifo "ukukhubazeka we-Duchenne-ERB." Ukwelapha eyenziwa onyakeni wokuqala wokuphila isiguli kancane, unika imiphumela emihle kakhulu. Ukusebenza Akayisusi izimpawu yenqubo sokugembula. It ikuvumela ukubuyisela indlela lapho ezinzwa amaza lihamba. Ngemva kwalokho kuboniswe ukwelashwa ngoludala usebenzisa elashwe ngokomzimba, massage.
Hlahluba okuzayo
Kufanele kuqondwe ukuthi ekwelapheni ukukhubazeka azoya - ke kuwumsebenzi othatha isikhathi futhi odinga isineke, kudinga isineke. iseluleko Zonke udokotela kufanele ilandelwe ngokunembile ukuze uthole umphumela omuhle. Abaningi nezinqubo zinwetshwe izinyanga, ikakhulukazi elashwe ngokomzimba futhi massage.
I ukukhubazeka kungase kuphele Duchenne-ERB: ukukhubazeka noma wokutakula? Ngeshwa, ukuze anikeze impendulo eqondile yalo mbuzo akunakwenzeka. Konke kuncike ezintweni ezifana:
- kobukhulu ukulimala;
- ukuhambisana nesikhathi kanye nokwanela yokwelapha;
- isifiso ukuba nizifeze zonke izincomo udokotela.
Uma unezilonda olulinganiselwe plexus brachial angaba nethemba lokuthethelelwa 100% yokutakula. Okungenani-ke uthi izibalo. Uma sekuphelile ngabodwa ithuba, ngeshwa, lincane kakhulu.
izinyathelo
Kungenzeka yini ukuthi luvimbele ukukhubazeka we-Duchenne-ERB? Izithombe izingane ezincane okwadingeka asebenzelane nalesi sifo, ngempela ukwenza ucabanga mayelana nalolu daba.
Eqinisweni, ukuvimbela izifo ulula. Litjho ukunakekelwa okufanele kwangaphambi kokubeletha, uzokhetha indlela kwezidingo. Ngisho esigabeni udinga ukuba banakekele icebo labo isimo, zama ukudla ngendlela efanele futhi ukwenze ezemidlalo sizikhandle. owesifazane enempilo kungenzeka ukuba babelethe ngaphandle pathologies. Ngaphezu kukhethwa isikhungo sezokwelapha lapho umama okhulelwe enquma zenzeka, kumele wasondela ngendlela efanele. Udinga ukufunda Izibuyekezo mayelana obelethisayo, inqubo ukulethwa kule emtholampilo. Ungase futhi uthintane nabangani asebethole ephethwe ukuzama ku indima kamama. Phakathi nenkathi yokukhulelwa kakhulu ezibaluleke ngqo ukulalela iseluleko udokotela wezifo zabesifazane, musa ukuyiziba izincomo zayo.
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