ImpiloIzifo nemibandela

Sarcoidosis - kuyini?

Mhlawumbe hhayi wonke wezwa yalesi sifo, sarcoidosis. Siyini ngempela lesi sifo ingatholakala kulesi sihloko. Sarcoidosis - ongavamile isifo sokuhlasela kwamasosha omzimba Lokudabuka engaziwa ukuthi kuthinta ngokuyinhloko umgudu wokuphefumula. Kulokhu, umzimba kwakhiwa granulomas - ekuqongeleleni okungavamile ukubulawa amasosha omzimba ahlasela inyama ephilile. I granulomas kuvame kwakheka lymph neuropathy yangaphakathi ISIZINDA, iphaphu, isikhumba, iso. Ngaphansi ngokuvamile, ziseZwini nezindlala izinso, isibindi, inhliziyo, amathambo, imisipha lwamathambo, ubuchopho, salivary. Kukholakala ukuthi lesi sifo nivame abesifazane engu-30 kuya kwengu-40.

Sarcoidosis. Siyini ngempela lesi sifo futhi yiziphi izimpawu zaso?

Ngokuvamile ukugula asymptomatic noma nge unezimpawu ezikahle. izimpawu ezinamandla akuvamile. Sarcoidosis libhekene ezihlukahlukene ukubonakaliswa zokwelapha, okuyinto incike indawo lesion.

Ezimweni eziningi (90%) enqubeni sokugembula kuhilela emaphashini, ngakhoke Isici esiyinhloko sifo - ukwandisa intrathoracic zamanzi. Kwezinye iziguli azikho izikhalo, abanye bangase babe a isifuba esomile, imfiva, ukuba buthakathaka kwezicubu, iphika ngesikhathi ukuvivinya umzimba, kanye umonakalo ezinzima emaphashini (esingamahlalakhona yamaphaphu, cystic).

Erythema nodosum uvame ukuhambisana nesifo ezinjalo, sarcoidosis. Yiziphi ezinye zalezi zimpawu? Ngokuvamile, ukubonakaliswa cutaneous lapho ngokuvamile ngesikhathi phambi shin kwakhiwa obukhulu, convex, ubuhlungu lapho sicindezelwe ISIZINDA umbala onsomi. Erythema nodosum libhekene ubuhlungu nokwephuka ngamadolo, ngenkathi kuqala, kukhona ubuhlungu emalungeni, futhi kuphela ngemuva ngokungabikho izinsukwana, kukhona ISIZINDA. Ukuba khona kwalawa izimpawu likhombisa izifundo evumayo kakhulu sarcoidosis.

Lapho lesi sifo kungase kube amehlo abathintekayo. Kulokhu, granuloma kwakheka conjunctiva. Ngokuvamile, iziguli esekhala ubuhlungu, ukoma, ububomvu, angaboni kahle. Late kutholakala ukuthi uphethwe yini sarcoid isifo samehlo igcwele ngobumpumputhe ephelele.

Ngenxa sarcoidosis iyisifo letindzala, kungangena nezinye izitho. Uma ukulimala kwezinso eba ezinso, inhliziyo - angina futhi inhliziyo ukuhluleka, umuntu pituitary indlala - sikashukela insipidus. angeke granulomas Hepatic kubonakaliswe ngezinye izikhathi imbangela izithelo zawo, imisebenzi umzimba ayagcinwa.

Sarcoidosis. nesigaba lesi sifo

Kususelwa radiographs kukhona izigaba ezintathu sarcoidosis yamaphaphu. Ngesikhathi kuqala amanothi izilonda zamazwe amabili ka intrathoracic zamanzi. Eyesibili libhekene lakhulisiwe lymph node kanye kokuziphatha nezicubu wamaphaphu ngaphandle cystic. Ngekhulu lesithathu kukhona evelele cystic kwamaphaphu ngaphandle ukwanda zamanzi. Isigaba sokuqala nesesibili ngokuvamile kwenzeka bessimtomno noma ukubonakaliswa extrapulmonary ube isicelo ejwayelekile, isib ukukhwehlela futhi dyspnea, bengekho.

Sarcoidosis. ukuhlola

Lesi sifo yokuthumela inqunywe-X-ray Ukuhlola Ukufiphaza isici yonkana isithombe kwesifuba. Granulomas kwakheka isifo sofuba yamaphaphu futhi, kocingo ke, ungaqhubeka lekufanele akhicitwe izicubu onesifo (biopsy), noma ukubeka tuberculin isikhumba test. Ngokuphathelene negazi, ACE serum (angiotensin ukuguqulela enzyme) anda sarcoidosis.

ukwelashwa

Ngokuvamile, i-Pulmonologist udokotela ephatha izifo ezifana sarcoidosis. Hlobo luni ukwelashwa? Uma uphethwe kuqinisekisiwe, udokotela eyonquma ngokusebenzisa kokuxilongwa, ngabe isifo kuvela kungenkathi evumayo noma ifomu asebenzayo. Ngokuhamba evumayo emitholampilo ukwelashwa is hhayi ngokuvamile kudingeka: nokuguqulwa self-ukuphulukiswa kwenzeka ezingaphezu kwesigamu amacala.

Uma inqubo ongahambanga ngale esifubeni, kubhekwa ziwuphawu oluhle. Ephambi kwezinduna isifo erythema nodosum siphela eminyakeni 1-1.5. Kwezinye izimo, ukusimama kuzothatha iminyaka eminingi, ngezinye izikhathi kufanele aphathwe ukuphila. Izibikezelo ayiyinhle, uma uye wahlakulela lokuphazamiseka okukhulu zokuphefumula, izinso wamshaya, inhliziyo, ubuchopho, futhi amehlo.

Nge ifomu asebenzayo lesi sifo ukuphathwa corticosteroids, okuyinto ukuqeda ubuhlungu bamalunga, iphika. Ngaphezu kwalokho, kusetshenziswa cytostatics, abacindezela ukubuyabuyelela engalawuliwe ukubulawa amasosha omzimba.

Iziguli kufanele belulekwe ukuze ngiyeke ukubhema futhi ukusetshenziswa carbohydrate acwengekile. Kufanele ngakususi imikhiqizo yobisi, ngenxa okuqukethwe eliphezulu calcium umchamo futhi igazi.

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