Marble isifo ithambo: izimbangela, izimpawu, ukwelashwa, zokuvimbela

Marble kuyinto azalwa naso isifo zokugula kubonakale osteosclerosis ehlasela umzimba kakhulu amathambo lwamathambo kanye izinguquko ekujuleni calcium-phosphorus umzimba. Lesi sifo ezingavamile kakhulu. Waqale ezichazwe 1904 by udokotela ohlinzayo isiJalimane radiologist Albers-Schoenberg (Albers-Schönberg NE). isifo Marble kwenzeka ngokuphelele kuzo zonke izigaba ubudala, emazweni emhlabeni wonke, ngokulinganayo zabo bobubili ubulili.

Lesi sifo enezinto eziningi omqondofana - osteosclerosis azalwa naso, osteopetrosis, futhi dysplasia giperostaticheskaya Albers-Schönberg isifo. Ungayididanisi isifo zemabula a syndrome ngokuthi "zemabula isikhumba." Lapho isifo zemabula amathambo asemzimbeni iqala ukukhiqiza extra izidakamizwa icwecwe, kanye umsele medullary ucala kutfutfukisa elicinene ithambo. A zemabula ngokuthi azalwa naso izitsha isikhumba vazonevroz esikhumbeni, ngokuvamile eziningi zenzeka izingane kubonakala izindawo reticular esikhumbeni umbala bluish ngemva eqeda. Ngemva ukufudumala uphawu iphele. Iphinde kwenzeka ngo abadala zemabula isikhumba nge isikhumba elincanyana ukukhanya abanezinkinga nemithambo yegazi.

Etiology yalesi sifo akwaziwa. Ezimweni eyaziwa kakhulu isifo it has a uhlamvu zemabula umndeni sisuka kwesinye isizukulwane iye kwesinye. Yakhe isifo igama zemabula ukweleta isithombe esikhethekile-X ray we skeleton, okuyinto okhonjiswe i homogeneity engavamile futhi abukhali kwamathambo, kanye ukuntuleka amathambo aqatha. Kubonakala sengathi amathambo zenziwa ngemabula.

Kukhona izinhlobo ezimbili zemabula isifo:

- eligeleza asinazo izimpawu ebonakalayo yomtholampilo, kwatholakala ukuthi nginesifo kuphela-X-ray luhlolo;

- kuzibonakalisa zisencane, ikhulumelani izimpawu.

Isici esiyinhloko sifo iyona ukuqina okuqhubekayo noma ngokwengxenye wethambo trabecular. Ngesikhathi besanda kuqala lesi sifo kuphela sclerotized amathambo ijabulise ku metaphyses amathambo flat ku izingxenye neuropathy. Ngaphezu kwalokho, itholiwe ukungalingani uphawu ithambo cranial, kakhulu abathintekayo ingaphakathi paranasal, eyinhloko ikakhulukazi futhi engaphelele. Ukunqotshwa siyalithola futhi omhlathi, kuhambisana ukwephulwa kuqhuma le ntaba, izinyo ukuthuthukiswa - ukushintsha isakhiwo sabo, izimpande insufficiently athuthukile, abhubhisa iziteshi kanye izimbotshana we izinyo. Ngokuvamile iziguli afune usizo lwezokwelapha imbangela nobuhlungu ezingalweni nasemilenzeni ukukhathala uma uhamba. Marble bamathambo futhi kubathinta kabi ukuthuthukiswa kohlelo semithambo, njengoba ukukhula ngokweqile normal ithambo izicubu kancane kancane ubuyisela izicubu hematopoietic.

Kuhle Imiphumela isifo ekwelapheni zemabula zazitholakala imizamo Ukufakelwa (Ukufakelwa) umnkantsha. ukwelashwa okuphumelelayo ngempela lesi sifo okwamanje zikhona. Ukwelashwa yalesi sifo ikakhulukazi kuhloswe ngazo ukuqinisa izinhlelo kwemisipha futhi ethukile, futhi kwenziwe ezimweni eziningi njengoba esibhedlela. Iziguli ukukhombisa Physiotherapy, massage and ukubhukuda. Nutrition kufanele kube ngokugcwele, ecebile izakhi trace kanye amavithamini, kumele kube khona kwimenyu, ushizi, imifino nezithelo ezintsha, izithelo zemvelo nemifino nesiphuzo. Izingane nale Ihlahlubo ethunyelwa ngesikhathi ukwelashwa kulesi sibhedlela.

Izindlela eziyisisekelo yokuvimbela isifo zemabula emayelana ubambe perinatal sokukhulelwa zokuxilonga amaviki angu-8. Ukuvimbela okuvela ithambo sengozini waphuka sokugembula kumele kwenziwe izivivinyo ashukumisayo e amathambo.