Impilo, Izifo nemibandela
Isifo sikaLou Gehrig, izimpawu yayo kanye nokwelashwa
SikaCharcot-Marie isifo libhekene okuqhubekayo yoma kwemisipha wemikhawulo aphansi. Ngokuvamile kuthinta imisipha distal of the imilenze. Lesi sifo libhekene Yiqiniso ezingamahlalakhona njalo (nakuba ngezinye igadango ezahlukene) ukuthuthukiswa. Naphezu uphethwe lula ngendlela efanele usaqala, ke ingenye esibi kunazo kuphazamiseka neurogenic.
Ubunzima kuphela ekutholweni yisiguli lesi sifo iyona iqoqo omqondofana, ekhombisa. Yingakho ngisho ukubeka ukuxilongwa udokotela kungahunyushwa akayena ngempela kuyiqiniso. Ngakho, omqondofana ezivamile: Lu Geriga syndrome, motor neuron isifo futhi ALS isifo - yesifo sokuwohloka kwezinzwa nemisipha.
izimbangela
Yiqiniso, izizathu ezinomthelela elivela kuzo izifo ezimbi kakhulu, azi kangcono ngekhanda. Okuwukuphela kwendlela ukuvimbela ukuthuthukiswa yabo. Kodwa, ngeshwa, isifo sikaLou Gehrig kuyinto esiwufuzo, okuyinto okubangelwa kuguquka amaprotheni ezimbili ezihlukene. Ngakho-ke, ukuze kuvinjelwe ukuthuthukiswa yayo umuntu akakwazi ukukwenza. Baphetha ngokuthini kuphela: kubantu abaphethwe akufanele babe abazali, njengoba amathuba abo okuba ingane enempilo usemncane kakhulu.
Njengoba isifo zako sikaLou Gehrig iqhubeka njalo futhi ningaphezi. Isizathu - umsebenzi omkhulu kakhulu kohlelo glutamatergic, odala acid oyinhlekelele izinzwa obhekene amandla kumiswa intambo izigaba umgogodla.
izimpawu
Njengomthetho, isifo sikaLou Gehrig kuzibonakalisa ebuntwaneni noma usakhula. Izimpawu zokuqala ukuthuthukiswa salo ukukhathala, ubuthakathaka, ukusinda futhi ubuhlungu emilenzeni, ushintsho ukuma ngezinyawo, i Gait engavamile futhi ungakhululekile, evula abuye avale emalungeni izinyawo kuyinkinga. Endabeni izimpawu okungenani eyodwa yalezi zimpawu kumele ngokushesha ukubona udokotela, njengoba izifo ezingaphezu dengwane, cishe wonke umzimba wesiguli.
Ukwazi kanjani ukuthatha impilo lesiguli, akunakwenzeka sokungabaza isidingo sokwelashwa. Phela, ngaphandle kosizo abaqeqeshiwe khona ithuba ngeshwa esihogweni. Futhi uma ekuqaleni isiguli uyozizwa kuphela ukungakhululeki kancane, isikhumba ngokuhamba kwesikhathi izoqala ukulahlekelwa ukuzwela, inqubo lasakazekela izandla, bese - ngakolunye imisipha yomzimba. Bayanda kuyoba nezinkinga nge umgudu wokuphefumula, ukukhubazeka olungaphelele nasemilenzeni kungenzeka. Isibikezelo akuyona ukuthi ayemakhulu amathemba ababenawo - phela ngenxa yezifo ezithathelwanayo kwamaphaphu noma amashubhu bronchial (futhi, mhlawumbe, e ukukhubazeka kwabo) isiguli uzofa.
ukwelashwa
Ngeshwa, isifo sikaLou Gehrig is hhayi ziphathwe. Odokotela kungenziwa kuphela izimpawu wakhe kanye nenqubekelaphambili kancane. Ukuze wenze lokhu, isiguli ebekiwe tonics, amavithamini, izidakamizwa ukuthi ngcono kwegazi imisipha. Imiphumela kungaletha eziningi umsebenzi zokwelapha, massage, futhi amasu wamathambo. Futhi-ke, iziguli eziningi bazodinga amaseshini owelapha, okuyinto uzokwazi ukubenza bakholwe ukuthi ukuphila namanje ungakaqedi, futhi kukhona njalo ngethemba.
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