Diathesis ukopha

Oluhambisana diathesis - igama abajwayelekile leqembu lezifo ezahlukene, behlanganiswe Isici esisodwa esifanayo - ukopha. Kukhona zombili izinhlobo zenani elikhulu eziyifa kanye kuluthola. Lapha isibonelo, izifo ezintathu ezahlukene kuleli qembu.

Oluhambisana vasculitis, okuthiwa futhi ngamanye izifo Henoch purpura. Lona ezivamile ukopha diathesis. Isizathu salokhu itholakala zokugula we microvascular izilonda ze-non-ethize, okuholela ukopha kanye nokuthuthukiswa thrombosis. Ngu ingqondo zici zihlanganisa ezibandayo, nokungezwani komzimba nezinto futhi umphumela ezidala. Kulesi isifo sibonakala ngezindlela ezine:

• umbani;
• Lesi siqhingi, engahlala kusuka amasonto ambalwa kuya ezinyangeni eziningana;
• nokunwetshiwe - ingahlala kusuka izinyanga ezimbalwa iminyaka eminingi;
• relapsing, ne isikhathi eside ukuthethelelwa esitebeleni.

Ukuqala njalo libhekene imfiva, kusukela kwabaneminyaka engamashumi amathathu nesishiyagalombili - degrees amathathu nesishiyagalolunye namashekeli kancane kancane kuyancipha ukuba subfebrile. Ngo parallel, uqala ukuvela purpura, lapho ngezinye izikhathi kunezindlela tincenye isifuba. Ngo isifo inzima izikhungo izakhi ukuqubuka zingavela foci of necrosis, bese - brown. Ngemva ukunyamalala ukuqubuka phezu lesikhumba isikhumba ngempela ukuhlala ezindaweni ezobonakala isikhathi eside. Kancane kancane, ubuhlungu emalungeni ezinkulu. Ezimweni eziningi, ikakhulukazi izingane, eba noma unomphela noma paroxysmal ubuhlungu besisu, okuyinto kubangelwa ukopha mesentery futhi odongeni emathunjini. Kubonakala ukuhlanza igazi. Okungenzeka bahlukunyezwe izinso glomerulonephritis uhlobo - noma oyingozi noma ezingamahlalakhona. Ngo umchamo, ngokulandelana, amaprotheni igazi livela.

Sifo kusekelwe umtholampilo isici. Laboratory luhlolo kufakazela eqonda intravascular coagulation syndrome.

Kanjani ukuze elashwe purpura diathesis-Henoch? Isiguli kumele esibhedlela ukuze saziso, esiqinile embhedeni ukuphumula okufanele sikhunjulwe okungenani amaviki amathathu. Ngenxa izidakamizwa esetshenziswa heparin, ascorbic acid kanye rutin. Contraindicated sulfa izidakamizwa, imithi elwa namagciwane kanye Physiotherapy. Akuvunyelwe ukudla ikhofi, ukhokho, strawberry, izithelo zohlobo lukalamula, iyiphi iziphuzo izithelo nesiphuzo. Esimeni buhlungu evelele emalungeni esetshenziswa indomethacin, analgin Brufen.

Haemophilia kuyinto diathesis ukopha, okuyinto ngenxa yokuntuleka Factor VIII emzimbeni futhi isici IX uhlelo of igazi ekunqandeni. Lesi sifo sibangelwa zofuzo ngocansi ku-X chromosome, okungukuthi isithwali - owesilisa nowesifazane indoda agule. Njengoba igazi ilahlekelwa amandla abo okuphila umlilo ihlule, isiguli singase sife cishe nokopha. ngaphandle ngopha izilonda, ukopha kwegazi ngaphansi kwesikhumba kungahle imisipha, kule ingaphakathi ngisho namalungu ezinkulu Kodwa.

Lokhu diathesis oluhambisana ezitholakala ebuntwaneni. Ngezinga akagcini ukopha kusuka isilonda enkabeni. I umchamo ngokuvamile utholakala hematuria.

Ukwelashwa luyabekezela igazi noma imithi yakhe, kanye Factor VIII ukugxilisa ingqondo.

Idiopathic thrombocytopenic purpura, noma thrombocytopenic purpura isifo. Kwande abesifazane. Lesi sifo lihlotshaniswa nokuncipha inani izinhlayiyana zegazi. Ngaleyo ndlela okubangela ukopha. Isizathu lesi sifo ngokuvamile kubangelwa izinkinga ne amasosha omzimba. Lesi sifo libhekene ukopha isikhumba, avame yenziwe yaba yasendaweni phezu imilenze kanye phambi kwesigamu umzimba, kanye endaweni umjovo. uphawu esisongela ebonisa ingozi ukopha ebuchosheni - is ukopha ulwelwesi emehlweni noma esikhumbeni. Izimpawu phusha ne amahanisi - omuhle. Kukhona kuwukwanda ubende.

Sifo kusekelwe imiphumela yomtholampilo futhi laboratory.

Ukwelashwa Kwenziwa prednisone kuzuzwe nomphumela omuhle, futhi wenza ukumpompela donor zegazi kanye igazi fresh.

Zonke lezi zifo iziguli ezisongela ukuphila, ikakhulukazi oluhambisana diathesis ezinganeni.