Butterfly syndrome: epidermolysis bullosa

Epidermolysis bullosa (Eb), noma njengoba ibizwa, butterfly syndrome - lena sifo esingavamile esidluliselwa ngofuzo kakhulu. Lezi zingane babizwa bona bantwana ne izimvemvane. Uma leli gama nivuna izinhlangano ezinye ezithakazelisayo, lesi sifo hhayi aesthetically elimnandi. Eqinisweni, iziguli ezinemishini epidermolysis bullosa ukuchitha impilo yabo yonke e buhlungu jeziso. Isizathu - isikhumba sabo, ezithambile njengalezo butterfly amaphiko.

Ngeshwa, lesi sifo singumbulali "butterfly syndrome" ayikwazi disinfected. Kungoba ngokujulile linamathele ezakhini zofuzo. Izingane ezinjalo badinge ukunakekelwa okukhethekile: imvelo ezithambile ngokuphelele, izingubo nezicathulo. ERussia, lokhu kuhle kwesifo esingelapheki esidluliselwa kungukuthi ngisho kufakwe uhlu izifo ezingavamile kakhulu. Nokho, kukhona isikhwama esikhethekile ukusiza izingane Butterfly "Bella."

Minyaka yonke imali eningi is zanikela esikhwameni, ukuze ngandlela-thile ukusiza izingane isifo "butterfly syndrome." Izithombe iziguli kungabonakala kulesi sihloko, futhi izincwadi zezokwelapha ezisekelwe ekwazisweni ngokwesayensi. Nokho, ulwazi epidermolysis bullosa akuzange wathola ukusatshalaliswa efanele eRussia kanye CIS amazwe.

Izifo "butterfly syndrome" akwaziwa umphakathi. Bambalwa kungaba amemezele ngisho igama layo kuyinkimbinkimbi - epidermolysis bullosa. Kodwa, laba bantwana babe kulo lonke elaseRussia kanye CIS amazwe. Ngamunye iziguli nge inkinga efanayo: odokotela bendawo awazi ukuthi bakwenza kanjani, uphethwe kuyinto "cishe", hhayi wahlala ethembekile izinhlobo zesifo. Futhi ngezinye izikhathi unina ngisho ukufihla lezi zingane, okuholela ekufeni kwabo ngenxa ukunakekelwa okungafanele.

butterfly syndrome libhekene ukubukeka komuntu ukuqubuka kwesikhumba bubble. Kuye Bubbles kukhona lezi zinhlobo ezilandelayo Epidermolysis Bullosa (Eb):

1. Simple. Kumiswa It is ezindaweni engenhla isikhumba. Isikhumba sikhula phezu neyamasundu amathe ezinyawo. Amagwebu zingase zimiswe ngisho emlonyeni.
2. Border. Kubonakala on kwalapho dermal-epidermal. Ngo nesifo esinzima Bubbles zingabonakala izindonga emphinjeni, amathumbu ipheshana genitourinary.
3. Dystrophic. Amagwebu ivele amadolo, izandla, izindololwane, nolwelwesi lwamafinyila, kungathinta emphinjeni, kubangele izinkinga zokukhula kanye nokudla. Lolu hlobo libuye libhekene Fusion iminwe yakhe nezinzwani zakhe.

Syndrome butterfly - umphumela kumiswa okungafanele amaprotheni esikhumbeni, noma ukungezwakali kwawo. Futhi imbangela sifo kungase kube into evele isakhi sofuzo wezakhi.

Ekuzalweni kwakhe, isikhumba ingane egulayo ilele njengoba isikhumba inyoka ehamba ngayo. Yiqiniso, lokhu kubangela ukusabela ukushaqeka e unina. Abaningi bamane senqabe izingane ezigulayo namanje e ewadini. Kodwa amathuba okusinda wengane nalesi sifo epidermolysis bullosa ekhaya zezingane cishe zero. Iningi izingane ushonele endaweni ukunakekelwa okungalungile. Phela, lezi zingane kudingeka asingathe ngokucophelela.

Inkathi eyayinzima kunazo zonke iziguli - lena engu kuze iminyaka 3. Kancane kancane, ngokunakekela efanele, isikhumba coarsens. A izingane ezincane uma uzama ukukhasa wonke amadolo bephundlekile futhi izandla. Skin amabhamuza kanye peels off, okubangela ubuhlungu obunzima. Izingane ezinjalo awukwazi ngisho Shake izandla njengoba umuntu ovamile. Nge esakhula, kancane kancane bafunde ukuze bazivikele. Lapho ngineminyaka engu-iminyaka engu-3 zokuphila iba lula.

Nokho, iziguli ezinemishini ifomu okunzima Epidermolysis Bullosa nsuku uhlangabezana ubuhlungu obukhulu ukulunywa, okuyinto ngeke kusize ngisho antihistamine. Ngaphezu kwalokho, njalo ngemva kwezinsuku ezintathu, kufanele ukukhuthazelela kusaladi ezidingekayo futhi kabuhlungu. Lezi zingane, njengazo zonke ezinye ogulela ukufa, kukhona ekhethekile. Banamehlo Amazing, cishe kusukela kule ubuhlungu obunjeya, asikwazi ukuqonda.