ImpiloImithi

Amyloidosis kwezinso: amafomu, izimpawu kanye nokwelashwa

Kunezindlela ezihlukahlukene of izinso izifo. Esinye sazo amyloidosis esiwumfanekiso sebethule amyloid ezicutshini. kwakhiwa Amyloid is in iziyaluyalu umzimba futhi ekhuthaza eziyinkimbinkimbi amaprotheni polysaccharides. amyloidosis kwezinso has izinhlobo eziningana ezinkulu:

1. eyisisekelo (engasasetshenziselwa iqanjwe amyloidosis idiopathic futhi genuinnogo), lapho imbangela sobala kunzima ukuchaza.

2. yesibili, okuyinto eyenzeka ngo-isizinda nezifo ezingamahlala khona.

3. zofuzo (ngofuzo, umndeni), okuyinto kuphakama ngenxa izifo ezibangelwa ufuzo wamaprotheni zamagama.

4. Senile

Njengoba umkhuba ubonisa, secondary amyloidosis kwezinso kwande ngaphezu eyinhloko. Kulokhu, isifo okubangelwa ivela khona, kungaba ezahlukene. Kungaba ukuthuthukisa ngenxa sofuba, osteomyelitis, kanye yizifo ezihlobene nokungabikho suppuration yamaphaphu. Futhi, lolu hlobo sifo livela samathambo, izilonda emathunjini. Ezimweni ezingavamile, amyloidosis kwezinso singenzeka ngokumelene isizinda sinusitis, namathansela, mastitis nogcunsula.

Ngokuvamile, amyloidosis kwezinso, izimpawu zingase zingaveli, has kungenzeka izici eziningana eziyinhloko:

1. ukubukeka puffiness

2. ubuthakathaka Periodic

3. Isifo sohudo

4. High blood pressure

5. ukwehluleka kwezinso

Ukuba khona amaprotheni ku umchamo - isici isici zonke izinhlobo amyloidosis. amyloidosis kwezinso kuholela ukuphazamiseka ukwehluleka inhliziyo futhi pheshana emathunjini. Ngokuvamile, dukane ezinzile enhliziyweni isigqi kwenzeka yokumelwa yinhliziyo. Nokho kukhona i isibindi lakhulisiwe futhi ubende, nakuba izimpawu ezikhanyayo ukusebenza kwabo kungenzeka ukuzibonakalisa.

Ukuze ukuxilonga amyloidosis kwezinso, ezidingekayo ukuze usingathe biopsy of izinso, isibindi, ikholoni nesikhumba. Ngokuvamile, i-biopsy emgodleni ingemuva e ezingaphezu kuka-70% of amacala kusiza ukuthola amyloid. Odokotela bavame biopsy omethembayo kakhulu.

Amyloidosis nayo eyenziwa echocardiography, okungase abonise uphawu kwesokunxele ventricle odongeni, septum phakathi ventricles, kanye izimpawu kahle umsebenzi diastolic. Ngokuvamile, kule isifo kwesokunxele ventricular ekamelweni osayizi evamile noma encishisiwe. Lapho ultrasound uqhutshwa, izinso Ubukhulu ngaleyo ndlela isifo kungenzeka evamile noma lenyuke.

imithi yesimanje ayinakho oluthile lokwelapha izifo ezifana amyloidosis kwezinso. Le nqubo yokwelapha, ngokuvamile ezisetshenziswa is, kuhloswe ngokuyinhloko at izimbangela oholele ukuthuthukiswa isifo (lokhu kusebenza ikakhulukazi ezimweni lapho amyloidosis kuyinto yesibili). Ngokuvamile, isiguli Kunconywa olukhethekile lokudla kanye Yiqiniso ngamakhemikhali. Ngezinye izikhathi hemodialysis futhi izinso ukufakelwa, okuyinto ubuyisela isitho onesifo.

Uma amyloids zitholakala kabi noma isiphi isitho esisodwa noma zasakazekela umzimba, amyloidosis akuyona esiyingozi ngenxa yokuphila isiguli. Izimpawu zesifo zikahle. Kungenjalo, yokutakula incike yokwelapha abakhethiwe kahle, ukushuba ukwelashwa nokugasela ngamandla kwalesi sifo oholele ukuthuthukiswa amyloidosis.

ukuphepha Impilo ukuvimbela ukuthuthukiswa isifo. Njengomthetho, ukuvimbela lesi simo ukwelashwa esifike ngesikhathi lesi sifo, engabangela umonakalo izinso kanye nokuthuthukiswa amyloidosis. Ngenxa yale njongo kubalulekile ukuba ibhekane nokuhlolwa odokotela njalo futhi ukuthatha ukuhlolwa ezidingekayo. Khona-ke ingozi yokuwohloka futhi okuvela isifo is kakhulu ziyancipha.

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