ImpiloIzifo nemibandela

Sezinso polycystic

Polycystic isifo sezinso kuyisifo esingathí sina esingase kakhulu futhi ezinzima, ngokuvamile inqubo ezimbili ngendlela, kodwa izinso okungenzeka bahlukunyezwe ngezindlela ezingafani. Lesi sifo kubonakala kunezindlela eziningi eliyingxenye kuwo womabili amaqembu izinso izinhlumba, okuyizinto anezikhwama round nge ketshezi aqueous. Cishe njalo, polycystic isifo sezinso eba khona yofuzo.

Izehlo izinhlumba ezihlobene ngokuqondile okuvela yokuphazamiseka of izinso tubules banesibopho umchamo okukhiphayo. Ngenxa yalokho, ezinye zazo ophela zifa, okuholela ukugcwaliswa ephelele ketshezi zabo, isb umchamo. Ngo operation evamile, izinso, umchamo ngemva kokuba hit in the tubules kwezinso ithunyelwa imbobo ukubuthwa, futhi kubo ngokusebenzisa izinkomishi ezinkulu nezincane izinso bese engena ureter ke excreted kusuka emzimbeni.

Ukuhlukanisa amafomu ezimbili eziyinhloko izinso polycystic ezihlukahlukayo uhlobo ifa. Ifomu yokuqala landile ebuntwaneni, bamthola umntwana, njengoba umthetho, ngokushesha emva kokuzalwa, wabiza autosomal polycystic esikhubazayo isifo sezinso, wesibili avame iqala abaneminyaka ephakathi kwengu-35-40 futhi ubizwa ngokuthi autosomal evelele polycystic nesifo sezinso. ifomu Autosomal evelele polycystic ihlangabezana zonke izakhamuzi senkulungwane iplanethi, futhi ingenye ezivame kakhulu izifo zofuzo. Kukhona azungeze 11-12 million. Abantu abaphethwe yilesi sifo. Ngo-90% autosomal evelele ifomu polycystic ngofuzo kubazali, asele 10% - umphumela yokwanda koshintsho nokuguqulwa.

Ngokuvamile, polycystic isifo sezinso sitholakale kubantu abaneminyaka ephakathi kwengu-engamashumi amabili kuya amane. Lesi sifo eba kancane kancane, cishe kusukela ekuzalweni, futhi imbangela enkingeni iqala kuphela lapho usukhulile. Lesi sifo esivela kokubili emadodeni nakwabesifazane ngokulinganayo, akunakwenzeka ukuba baqaphele futhi ukuhlukanisa kunoma yiliphi iqembu labantu, nalesi sifo kaningi kunabanye.

polycystic isifo sezinso: izimpawu.

Ngeshwa, owokuqala izimpawu of polycystic isifo sezinso kunzima ukuvumelanisa ngayo isifo: high blood pressure, ukukhathala, ubuhlungu buthuntu esifundeni lumbar, iziyaluyalu esimiso senhliziyo nemithambo yegazi, ukuchama kaningi, ngokuvamile okuxutshwe negazi. amafomu Advanced ephelezelwa ukubukeka iqhubu polycystic esiswini. Ngokuvamile anganele kuye njengoba pyelonephritis isifo co ezihlobene, okuyinto kudala izimo ezikahle ezifanelekayo ukufuya Amagciwane.

Endabeni ka umonakalo omkhulu parenchyma, iziguli umuzwa oqinile ngenxa yokoma futhi kudla imali enkulu yamanzi, lapho ethintwa yimizwa izinso polycystic ingasakwazi ngokwanele ukugxilisa ingqondo umchamo. Waba yini umphumela walesi ukwehluleka iyona bheke ephelele cishe zakho konke emuva ketshezi.

Ingozi main kuyinto ukuthuthukiswa polycystic isifo sezinso, lapho izinso abakwazi nje kufanele yenze imisebenzi yabo.

polycystic isifo sezinso: ukwelashwa.

Ikakhulu ukwelashwa ngoludala lesi sifo kuyehla kube ulwe nesifo esingamahlalakhona kwezinso futhi ukutheleleka yesibili nezinso. Phambi yezinkinga ezifana ngokukhukhumala kwentamo glomerunefrit esimisiwe hormone steroid futhi khona nomfutho wegazi ophezulu - antihypertensives. Kwezinye izimo ukuphathwa kuhlinzwa Kunconywa, okuyinto resection ahlukene izimbotshana fibrosis emelela isimiso mechanical umchamo outflow futhi ukukhuthaza Ukuwohloka perfusion kwezinso. Ngaphezu kwalokho, iziguli kufanele ugweme ngokweqile kokuvivinya umzimba, kunyakaze, ibanga elide, kufanele siqaphe ukuba imikhuhlane kanye nezifo, sihlale njalo siqaphele isimo namazinyo nomphimbo.

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