Lesi sifo-cystic fibrosis. Kuyini lokhu?

cystic fibrosis mhlawumbe isifo ovamile kakhulu emhlabeni, sitholwa njengefa. Waqale esachazwa wezingane American uDorothy Anderson ngo-1938 Igama olusemthethweni - cystic kwamanyikwe.

cystic fibrosis: kuyini?

Ukuvela ochwepheshe isifo elihlobene ne ngokuguqula izakhi iprotheni yenza umsebenzi chloride isiteshi futhi babehileleke amanzi electrolyte ibhalansi ezitokisini zokuphefumula, pheshana emathunjini, amanyikwe, uhlelo urinary nesibindi. Lapho izinguquko ezingenakuhlehliswa amaprotheni zichithe semali wangaphandle uketshezi nezindlala wafingqa kakhulu, kuba nzima ukuba kude kwaso, kukhona ukuphazamiseka izitho zangaphakathi. cystic fibrosis kuthinta kaningi ke uhlelo bronchopulmonary.

Imithambo yegazi achazwayo ukuvuvukala ezinzima ezihlukahlukene gravity ehlala uzimele exhumanisayo, nezimvula bronchiectasis akhiwa ngokushesha. Ngezinye njalo wokufaka ngempela viscous isikhwehlela bronchiectasis ayabaluleka njalo, ekugcineni okwandisa hypoxia kanye nomfutho wegazi ophezulu yamaphaphu.

cystic fibrosis: kuyini futhi yiziphi izimpawu?

Kuyaphawuleka ukuthi izimpawu zesifo kungahle kungabi ngokushesha. Odokotela bavame ukuqala ukwelapha ukucinana kwemigudu yokuphefumula abajwayelekile, kodwa ukuphela kwayo kamuva kuvela ukuthi lokhu akunjalo, futhi-cystic fibrosis. Usizo ke uhlamvu ehluke ngokuphelele. Abaphethwe isifo libhekene:

• a lag abalulekile ekuthuthukisweni ngokomzimba;
• izifo kwezitho zokuphefumula (kuhlanganise sinusitis kanye ukucinana kwemigudu yokuphefumula);
• polyp ku ekhaleni;
• pancreatitis;
• nokuvaleka kwemigudu yokuphefumula.

cystic fibrosis: ukuthi kuyini futhi kanjani it kutholakala ukuthi uphethwe yini?

Yiqiniso, yokuqondisa uphethwe yini ngaphandle luhlolo efanele abanakukwazi ukwenza. On inkinga kangcono ngendlela edidiyelayo. Assays zazo ebekiwe ukuthola cystic fibrosis:

• ujuluke ukuhlolwa;
• chloride okuhlushwa;
• chymotrypsin e kwesihlalo;
• fatty acid e kwesihlalo;
• ukuhlola DNA.

cystic fibrosis: ukuthi kuyini futhi kanjani it iphathwa?

Okwamanje, ukukunqoba ngokuphelele lesi sifo ayinakwenzeka. Kodwa uma ukunakekela iziguli ezine-cystic fibrosis enikeziwe ngesikhathi, ngisho nale uphethwe umuntu angaphila ukuphila sasivumela eside.

Zonke iziguli iphathwa kuyinto ukudla izinga nomsebenzi ngokomzimba. Ukudla umthwalo amasethi uchwepheshe ngamunye. Khona-ke ekwelapheni fibrosis cystic ukuqhutshwa, esekelwe izimpawu. Injongo eyinhloko yawo odokotela lapha - ekuvimbeleni ukuvaleka emaphashini futhi kuvimbele ukuvimbela pheshana emathunjini. Zonke iziguli ngesikhathi esifanayo zibhaliswe ku Dispensary.

Basic kadokotela: enzymatic, anti-fungal namanxusa elwa namagciwane. Njengoba ngokuvamile ukwelashwa ngokomzimba kuyabekwa vibration massage yonkana esifubeni kanye yokuzijwayeza ekhethekile.

Ingabe ikhona indlela savela ngengozi?

Ngokwemibiko ethile isilinganiso sobude bokuphila isiguli eRussia - iminyaka 15-18. E-US, isibonelo, nge kokutshelwa ngokukhubazeka kwengane isiguli uhlala okuyisilinganiso seminyaka engu 28-42.

Kodwa imithi, njengoba sazi, akemi namanje. Ososayensi emhlabeni wonke le sifo uzifunde ngokucophelela. Kukholakala abaningi kulezi ziguli, ababezalelwe 2000, ezokwelapha zesimanje kungaqinisekisa ngokugcwele uNkulnkulu 45-55 nokwanelisayo.