Impilo, Izifo nemibandela
Kuyini Gardner syndrome?
Kukhona pathologies eziningi zizuzwe futhi abekwa ezingeni zofuzo. Noma kunjalo, ezinye zazo akuzona ngokushesha, kodwa kuphela lapho usukhulile. Phakathi izifo ezifana Gardner syndrome. Lokhu zokugula libhekisela izimila kungavamile ukuba ingozi, ngezinye izikhathi enokuthambekela umdlavuza, okusho ingena umdlavuza.
Incazelo Gardner syndrome
Lokhu zokugula liye laziwa muva. Waqale ezichazwe nekhulu lama-20, ososayensi Gardner. Nguye kusungulwa ukuxhumana okukhona phakathi zokwakheka ingozi kwesikhumba, amathambo, futhi ipheshana wokugaya ukudla. Enye igama isifo - kuba umndeni (noma lezinceku) polyposis adenomatous. Gardner Syndrome wesabeka hhayi kuphela eminingi yezimonyo in sesikhumba zamehlo. Kukholakala ukuthi polyposis ikholoni iba ifomu ebulalayo e 90-95% of amacala. Ngenxa yalesi sizathu, i-pathology kubhekwe ukuphoqa izilonda precancerous. Imiphumela yaloku kuhlola okungenhla umehluko Kwenziwa atheroma syndrome Riklenghauzena, osteomas olulodwa futhi polyp emathunjini.
Izimbangela lesi sifo kanye indlela yentuthuko
Gardner Syndrome kubhekisela esenzakalweni esiyisimangaliso zokugula sitholwa njengefa. It is adluliselwa ngofuzo kubazali amanye amalungu omndeni (ugogo nomkhulu). uhlobo ifa zesifo - autosomal evelele. Lokhu kusho awokuthi yizifo kubazali nezingane. At inhliziyo Gardner ukuthuthukiswa syndrome mshini dysplasia mesenchyme. Ngoba kwakhiwa le ndwangu yi esikhumbeni, ethanjeni mucosa yokusetshenziswa pheshana emathunjini, kukhona isici ukubhebhetheka kwalesi sifo isithombe emtholampilo. Ngaphezu zofuzo nezici ezithile mesenchymal dysplasia zingase zimiswe bedle izici eziyingozi ezithinta ukuthuthukiswa kokubeletha ngesikhathi senyanga yokuqala sokukhulelwa.
Gardner Syndrome: izimpawu
Ngokuvamile, isifo kubonakala entsheni (iminyaka engu-10). Kwezinye izimo, izimpawu zokuqala uqale kamuva - kakade ekuphileni omdala. Gardner Syndrome has miphumela elandelayo: kuba izimila isikhumba, izicubu zomzimba ezithambile, ethanjeni wokugaya ukudla. Ngaphezu polyp emathunjini kungenzeka esiswini duodenum. On the isikhumba kungabonakala nasemkhakheni atheroma, dermoid futhi izinhlumba sebaceous, fibroids. Kungenzeka futhi ukuvela izicubu zomzimba ezithambile kungavamile ukuba ingozi. Lezi zihlanganisa lipoma futhi leiomyoma. Zonke lezi izimila singenzeka ebusweni, ekhanda, izandla noma izinyawo. Ngaphezu kwalokho kukhona ithambo izilonda. Futhi basonta kungavamile ukuba ingozi, kodwa ngokuvamile kunzima umsebenzi. Ngokwesibonelo, osteoma ithambo we umhlathi ongezansi, Yekhanda. Lezi neziqu ukugxambukela betel angase acindezele isakhiwo ingqondo. Ukubonakaliswa esibi kakhulu lesi sifo singumbulali polyp wamathumbu nezinye ipheshana wokugaya ukudla. Ezimweni eziningi, izimila ipheshana yesisu nolwelwesi lwamafinyila maligniziruyutsya, okusho ujike abe umdlavuza. Polyp kungaba isikhathi eside ukuba kuthintwe. Ngokuvamile, iziguli akhononde izinkinga ngemva kokuhlinzwa, ukuvimbela emathunjini, ukopha.
Gardner ukwelashwa sifo ngo-Cuba: izinzuzo
Njengoba isifo kuyinto precancer baphoqwe kudingeka ukususwa kuhlinzwa izimila. Kubalulekile kakhulu ukuxilonga Gardner Syndrome. iziguli Photo kungabonwa izincwadi yomdlavuza, noma amasayithi ekhethekile. Ngaphezu ukubonakaliswa emitholampilo kuyadingeka ukuze ukuqhuba esimweni ka ipheshana wokugaya ukudla, colonoscopy. Kuvela izilonda zesikhumba nokushintsha polyposis emathunjini uvumele ithole ukuxilongwa okufanele. Gardner ukwelashwa syndrome wenziwa emazweni amaningi. Izinzuzo imitholampilo-Cuban zihlanganisa imishini yamuva, izindleko nokusebenza kuhlinzwa, kakhulu ochwepheshe abafanelekayo kusuka emhlabeni wonke. I kwelashwa ukususa ingxenye ethintekile wamathumbu. Ungase futhi ukuqeda yezimonyo in sesikhumba zamehlo.
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