ImpiloIzifo nemibandela

Ichthyosis isikhumba: izimbangela, izimpawu, ukwelashwa

Medicine labelwe iqembu ahlukene izifo, okuyinto kubangelwa izinguquko ungqimba olukha phezulu isikhumba ezakhini zofuzo. Ngenxa yokwephula kwesikhumba sibhekana nezinguquko ezithile futhi uyofana amazenga enhlanzi. Lesi sifo sitholwa njengefa futhi kungaba ukuzibonakalisa ngasiphi umuntu ubudala, kungakhathaliseki ukuthi abaluphi uhlanga, ubulili kanye nesimo nomphakathi. Ichthyosis ungaboniswa kabi futhi hhayi anikezwe isiguli izinkinga futhi kungaba nolaka ngisho ziholele ekufeni. ichthyosis futhi ichthyosiform isikhumba izifo izinhlobo isisindo futhi, ngeshwa, ezijwayelekile futhi kunzima ukuyelapha. okuholela laboratories abaningi bezokwelapha abasebenza kanzima ngandlela-thile ukunqanda zokugula futhi wenze ukuphila kube lula ukuze iziguli.

Kuyini ichthyosis

kumiswa okungavamile we corneum stratum - ichthyosis. izimbangela zako ziyizindlela ngenxa kwezinso e ikhodi zofuzo oyedwa noma bobabili abazali - okungukuthi, e X-chromosome. Kukhona izifo eziningi azibonakali futhi ibukeke ichthyosis, kodwa empeleni akuzona. Ngenxa yokwethuka ekukhombeni at nezimpawu ezifanayo akudingekile. Lesi sifo ngempela kungase kwembule kuphela onguchwepheshe, futhi iningi lawo afana izifo zesikhumba usulaphekile ngempumelelo. ichthyosis futhi ichthyosiform esehlaselwa isifo sesikhumba esenyanyekayo babe nezinkolelo ezihlukahlukene zezinhlanzi, kodwa umuthi ngokusemthethweni lubahlukanise ngemacembu eziningana. Funda kabanzi mayelana ngamunye kubo - ngezansi.

ichthyosis abavamile

Futhi kubizwa ichthyosis vulgaris, ke ingenye lwezinhlobo ezivame kakhulu. Lesi sifo kubonakala esemncane, kodwa ngokungafani nezinye izinhlobo, akusho ushaye izingane ezingaphansi kweminyaka 3 izinyanga ubudala.

Lesi sifo ezinodlame kakhulu liziphatha ngesikhathi nokuvuthwa zocansi esiguli, futhi imayelana 10 ubudala. Uma ama-hormone ekulinganiseni umuntu, ziza futhi ngcono isimo sesikhumba. Ezinye impumuzo iza isizini ihlobo, kodwa abandayo snap isifo iqala ukuba bathuthuke. Bafana namantombazane nge amathuba alinganayo angagcina lesi sifo. ichthyosis abavamile idluliswe kusukela yenethiwekhi (omunye umzali) ingane. Lesi sifo olandela nesineke kukho konke ukuphila, isimo kungathuthukisa futhi siba sibi.

Izimpawu ichthyosis vulgaris

Ichthyosis vulgaris uthola igama layo kusukela lokuthi wayebonakala ababukisa ngakho. Lesi sifo zithinta isikhumba, izihlathi, ebunzini nezindebe wabuka ikakhulukazi. Isikhumba embozwe izikali ezincane olumhlophe iso sobala kakhulu. Umbala wawo futhi lesi sijame njengebhoksi kakolweni bran, ngoba ichthyosis ngokuvamile enjalo kwesikhumba ibizwa ngokuthi "pityriasis umbandamu". ezindaweni ezithintekile awekho ngaphansi reddening noma ukuvuvukala, kodwa isikhumba uba omile futhi olungaqinile. Lesi sifo akuphazamisi izinwele noma izipikili omdala nesineke futhi akazange kumenze izinkinga ezinkulu.

Ubuso - kuphela endaweni yokuqala yendawo, ngokuhamba kwesikhathi, flaking senzeka ngokuphelele, kodwa iye yabathinta nezinye izindawo emzimbeni. Ngokuvamile kuba nedolo endololwaneni, ezinqulwini endaweni emuva aphansi, ngezinye izikhathi iqakala. Lokhu akuthinti ichthyosis, ngokungafani nezinye izinhlobo, imbilapho endaweni futhi ibeka emphethweni isikhumba ezinkulu. Ngu uhlobo sifo kanye ubukhulu kanye ukuma ishq evamile isikhumba ichthyosis zihlukaniswe izinhlobo eziningana: ichthyosis elula, xeroderma oyinyoka, inaliti, omnyama acwebezelayo (pearlescent) ichthyosis.

nezindaba ezihlobene

Izingane ezincane nabantu intsha esanda ichthyosis ngcolile. Izizathu njengoba ukwephulwa kwezitho zomzimba.

  • Ingane kancane ezikhulayo noma ikhula ngesisindo esifanele, ubukeka emincane, ngeziphambeko sokukhula kwengqondo.
  • uketshezi kwamakhono sebum nomjuluko phetho - sinqamukile isakhiwo izinwele, bangakwazi fall out. Nail amapuleti naba buthuntu, zondile futhi ziyaqothuka.
  • Buthakathaka amasosha omzimba, futhi ngoba izingane ngokuvamile uhlushwa izifo ezibangelwa amagciwane kanye ukuvuvukala.
  • umzimba Disturbed futhi hormone yegilo umzimba.
  • I-cholesterol igazi liphuma, okungase ke kuholele izifo zenhliziyo kanye semithambo uhlelo.
  • Thuthukisa "ukungaboni" - isimo lapho abantu musa ukuhlukanisa izinto ebumnyameni.

Zonke lezi zinkinga sobala ikakhulukazi the nobusika. Kuyadingeka ukuba unake okukhethekile ukungondleki kanye nempilo. Ziwusizo umoya opholile kanye nokuphumula ilanga.

ichthyosis Ordinary ifomu esikhubazayo

Lesi sifo ichthyosis esikhubazayo efomini lokubonakala ukubonakaliswa okunamandla zesikhumba uyaxebuka kuyo yonke umzimba futhi bahlanganiswe ngobulili: ahlupheke leli fomu abameleli besilisa kuphela. Girls kuyaqabukela agule, kodwa kukhona abathwali. Njengoba omama, bona adlulisele isifo namadodana akhe, okwathi ngemva kwalokho adlulisa chromosome lezinceku kanjalo amadodakazi abo. Ngakho ungaqhubeka okwesikhathi eside.

Emantombazaneni ifomu esikhubazayo lesi sifo kungaba yingozi. Ezimweni ezinjalo ezingavamile futhi kungenzeka kuphela uma abazali bakhe bobabili baye bangenwa ke uyonikwa pathologic X chromosome indodakazi. Lesi sifo kakhulu, la mantombazane kuyaqabukela ukusinda.

Izimpawu ifomu esikhubazayo

Kakhulu ngokuvamile abathintekayo sezinwele, izinwele thinning, baphume, kungavela impandla ephelele. Ishq emikhulu futhi obukhulu, ngokungafani amafomu inhlamba ziba nombala mnyama. Iziguli iziyaluyalu kwezitho. Kwangathi ukuthuthukisa ithambo iziyaluyalu futhi retardation engqondo, corneas esinamafu, kukhona amacala isithuthwane.

ichthyosis azalwa naso e ezinzima

ichthyosis azalwa naso - the zokugula eziyinkimbinkimbi kakhulu, kungase kube okuncane noma okukhulu. Amaphesenti sokusinda lincane kakhulu, izingane zibulawa kungakapheli amahora ambalwa emva kokuzalwa. Ezimweni ezingavamile, ingane uphatha ukulondoloza. Lesi sifo iyaguquguquka kumafomu ezahlukene, erythroderma, isibonelo. Ezimweni ezingavamile kakhulu, okuyinto Ingabizwa kufanele ngokuthi isimangaliso, lesi sifo zivame ukufiphala ngokuphelele ngobudala indoda nakakhulu ukukhathazeka.

Izimpawu ezinzima

ichthyosis azalwa naso ezinganeni kuzibonakalisa eziningi iziyaluyalu futhi kombungu. Lezi zingane zizalwa kwesikhathi, nge isisindo sokuzalwa. Isikhumba sengane yahlehla sifana zempi, onikeza imifantu futhi oozing igazi.

Ngesikhathi lapho sinqamukile ukuthuthukiswa isikhumba kwengane, nezinye izitho zomzimba, izicubu isikhwehlela ukuqhubeka ukuthuthukisa evamile. Isikhumba akuyona nokunwebeka, ngoba kunesithembiso abese ephinda ebasa enamathiselwe indwangu ngaphandle. Ubuso nazo zonke umzimba wengane kanzima zikhubazekile futhi uthathe i ukubukeka nemvelo.

Isizathu sokuba okusezingeni eliphezulu lokufa e izinsana ngenxa yokuthi ukuthi into yi-keratin ikhulisa bese idonsa noma ngokuphelele clogs izitho ezibalulekile. Newborn akakwazi ukuphefumula futhi udle, izitho zangaphakathi obungefani ekuthuthukisweni, ukutheleleka okuhlobene. Lezi zingane zibizwa ngokuthi "Harlequin", futhi isifo - ". Harlequin uphawu"

ichthyosis azalwa naso omnene

Uma ichthyosis azalwa naso eba omnene (ingozi) ifomu, izinyane uthola ithuba lokuphila. izicubu Keratinized ikhula ngisho ifomu ezinzima. izitho zangaphakathi ngisho noma zikhubazekile, bayakwazi ukufeza umsebenzi zawo ezibalulekile.

Izimpawu imnene

Ichthyosis ezinganeni kungathinta wonke isikhumba, noma izigaba ezithile kuphela. Ezindaweni ezinjalo, isikhumba kuba obomvu, edematous palpated ngezansi uphawu, ikakhulukazi ezindaweni lapho imibimbi isikhumba. izindawo sokugembula ebusweni kungenzeka banyakamisa ukubukeka, ezimazombe zamabhodlela noma ikhala nomlomo ndawo. Kodwa amathuba okusinda kulezi izingane.

Ichthyosis ngefomu "brilliant"

isikhumba okunjalo ichthyosis ngezinye izikhathi udidekile ne zoster izinwele. Kubonakaliswa izingxenye lapho isikhumba uzimisele (amadolo, indololwane amalunga omzimba). Foci embozwe Izigaxana ezincane ukuthi isipikili izikali ezinkulu shiny onsomi.

zokuvimbela

Ichthyosis - isifo sesikhumba angeke kuvinjelwe, kodwa kungenzeka ukuba sibikezele sokuzalwa kwezingane nalesi sifo. Kube eziningi zokuhlela izikhungo umndeni ukuthi beluleke zofuzo. Ochwepheshe ngeke ikhumbule zonke nemingcele, ikakhulukazi uma umbhangqwana osemusha noma izihlobo zabo kuye kwaba namacala ichthyosis. Ufuzo ngeke uqhathanise izindlela futhi izingozi ezingaba khona kwezifo okunzima ku-fetus futhi unike izincomo ephathelene nekusasa ukuhlela ingane. Uma izingozi ziphezulu, lokhu pair kungase kube ukuhlakanipha ukuba bangayeki lokuzalwa kwengane. Kodwa noma ngabe kunjalo, isinqumo kuzoncika kuphela abashadayo.

isifo ichthyosis ngefomu ezinzima - nobulwelwe kakhulu. Ukufa kwezinsana cishe 100%. Ngisho noma ingane yakho futhi bakwazi ukusinda, akunakwenzeka ejwayelekile ayeziphilisa kungenziwa ngokuthi ukhululekile. ingane enjalo ngeke bakwazi ukuthuthukisa evamile. Iyoba kuncike comorbidities eziningi, konke okwenzayo ngeke babangela ukuhlupheka ngenxa yobuhlungu. Abantu abashadile kumelwe ubonise umthwalo futhi ukuba bangakushayi indiva iseluleko ochwepheshe.

ukwelashwa

Uxilongwe "ichthyosis"? Kanjani ukwelapha lesi sifo? Ohilelekile ekwelashweni nokulawula Yiqiniso lesi sifo, dermatologists, izazi zezakhi zofuzo, odokotela nezifo ezithathelwanayo. Ngokudabukisayo, lesi sifo libhekisela izifo ezihlukahlukene zofuzo, futhi kuyinto engenakwenzeka ukuba uthole ngokuphelele ukuqeda kwalo. Medicine ungakwazi kuphela balondoloze izinga lokuphila isiguli ezingeni elifanele futhi kuzo zonke kuphazamise ukuvela izifo. Cream namafutha ezokwenza ukuthambisa zokukhipha igciwane ezindaweni ezithintekile, iziguli ziyophoqeleka ukusebenzisa ukuphila kwabo konke.

isifo ichthyosis liyinkimbinkimbi nasengqondweni. Ungase udinge izazi zokusebenza kwengqondo, kanye nokwesekwa kubalulekile labangani asondelene nabo. Ukwenqatshwa umphakathi ungakwazi sicindezeleke isimo esinzima kakade lomuntu. Izingane kudingeka ukuxhumana nontanga yabo. Kubalulekile ukuchaza izingane ukuthi lesi sifo asithathelwani futhi akuyona ziyingozi kuzo.

Kuyadingeka ukunakekela. Amandla kufanele kuphelele. Sunbathingkuva, kodwa qiniseka ukugwema ukushiswa ilanga futhi okweqile. Ibonisa ukugeza emanzini olwandle noma ukugeza ngezinsalela uLwandle Lukasawoti. Kuyadingeka ukuba silondoloze enempilo futhi ngesikhathi ukugula kancane ukudinga odokotela. Lesifo kancane singena emzimbeni buthakathaka, uyakwazi ngokushesha luphenduke isifo esitalini ukuxakeka.

izindlela Traditional nokwelashwa ichthyosis

Abelaphi aluleka nenqwaba kulabo abaphethwe zibe maholoholo isikhumba. Bonke ezahlukene futhi befanele ngandlela-thile ukudambisa isifo ukunciphisa ukungakhululeki. Nokho, khumbula ukulandela iseluleko abantu abavukwa ukuhlobana ezingabazekayo kokwelapha, ngokuqapha kumele kusetshenziswe. Uma ugogo emakethe kuyoba kuyisidina agxumele wena izidakamizwa "kusukela Izilonda ichthyosis Shleymana", okusho ngokwemvelo alikho, kungcono ukugcina kusukela kule "intern" kude. Kodwa imithi khona ngempela ukuma izincomo. Ngokuvamile, lezi zezinkambi namabhati phezu decoction yamakhambi. Zikhona izindlela ekhaya yokugcoba ezigxile hydration, umsoco kanye isikhumba magciwane. Bonke yenziwe ngezithako zemvelo, upheke kubo ekhaya kulula. Mhlawumbe uzothola bazikhethele izindlela ezimbalwa ngempumelelo futhi elula.

Ngenhla Ukufuna ikhambi kubantu abaphethwe izifo zofuzo, umsebenzi zofuzo futhi laboratory emazweni amaningi. Ake bathemba ukuthi ikhambi lizotholakala maduze, futhi siyokwazi wokuqeda isintu isifo kabi ngisho okunjalo okuyingozi.

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