ImpiloIzifo nemibandela

Henoch sika isifo: pathogenesis, izimpawu, ukuthola

Oluhambisana vasculitis (Henoch-Schonlein purpura isifo) kungokwalabo diatheses atholwe okubangelwa ukwanda esasiyomzuzisa permeability izindonga isitsha. Kukhona izinhlobo eziningana ukubonakaliswa yayo. Igama elithi "Henoch-Schönlein" ukuya phesheya. Igama elithi "vasculitis gemorrragichesky" isetshenziswa kuphela ku imithi yasekhaya kusukela 1959.

isifo Henoch sika: pathogenesis

Kusekelwe yisishiso iguliswa yegazi amancane ama-capillary. Ngenxa yalokho, it exuded plasma bese zamangqamuzana abomvu egazi ise nezicubu eziseduze. Histopathological izilonda isithombe cishe kuyafana periarteritis nodosa. Kodwa labo imikhumbi kabana oluhambisana vasculitis, ngisho ezincane.

isifo Henoch sika: izimpawu

Kuthinta abantu ikakhulukazi abasha. Oholela uphawu - ukuqubuka phezu imilenze nge uhlamvu exudative-oluhambisana. I Izigaxana kungenzeka lobehlukene, kodwa ngokuvamile ezincane afanako ngokufanele. Ukuqubuka uvame ukuhambisana ubuhlungu bamalunga, ukulunywa, ukucobeka ukunyuka kwezinga lokushisa iyonke. Uma lesi sifo kunzima kakhulu, ngalesosikhathi embula uphinde uhlangane ku oluhambisana izindawo ezinkulu. Ungezwa opha ukufa izindawo ebanzi. emva kwezinsuku 10-15 ukuqubuka ngokuvamile buphela, kodwa hhayi kuze kube phakade. ke lihlala livela kaningi. Ngenxa edema periarticular, eshintsha emalungeni. Ngezinye izikhathi isifo Henoch sika sishubiswa ngokwengeziwe ukopha ezicutshini futhi izitho zangaphakathi. Uma kwenzeka ngokuhamba esiswini namathumbu, esiswini kokuba sezinhlungwini abukhali. Ubuchopho ukopha kuhambisana ukuthuthukiswa ukukhubazeka kanye paresis. Ngezinye izikhathi izinguquko ejwayelekile oluhambisana vasculitis, kwenzeke hhayi kuphela izitho zangaphakathi, futhi imithambo yegazi retina futhi kuthinte amehlo futhi uqondiswe isimiso sezinzwa esiyinhloko.

isifo Henoch sika: ukuma

Ziyakwazi ezine: samathambo umbani-fast, kulula, futhi besisu purpura. Ngamunye wabo inezimpawu yayo eqondile. purpura Simple, isib, ephelezelwa ukuqubuka oluhambisana esikhumbeni futhi nolwelwesi lwamafinyila. Ivela ukucobeka jikelele, izinga lokushisa likhuphuka. Ngo-rheumatoid purpura izinguquko zenzeka emalungeni (ngokuvamile kwedolo). Njengoba eqhubeka ehamba aba buhlungu kakhulu, zigcwala. Ezijwayelekile e intsha nezingane kwenzeka purpura besisu. Lapho kuphakama ukopha emathunjini bese esiswini. Ubuhlungu obukhulu besisu kukhona ukuhlaselwa. I ebuhlanzweni waphawula admixture wegazi, hlalani indle. Zonke lezi zenzakalo ahambisana ukunyuka kwezinga lokushisa komzimba. Ngesikhathi esifanayo lapho futhi isici ngamawala. Ngaphansi ngokuvamile sibandulele besisu syndrome noma kwenzeka ngemva. purpura Fulminant has izimpawu ezifanayo, kodwa ngokuvamile kunzima kangangokuthi ukusuka ngezinsuku zokuqala kungaphumela ekufeni.

isifo Henoch sika: ukuqashelwa

Kubalulekile ukwehlukanisa ke kusukela hemophilia futhi purpura thrombocytopenic. Recognition kusekelwe khona ethize kanye owaziwa exudative oluhambisana amawala, izinhlungu ngokuhlanganyela lemikhuhlane bebonke. Uma ucabangela Imiphumela yalolu cwaningo kufanele bacabangele inani zegazi - abayikho evamile, akukho izinguquko okudingeka abe izinkomba wegazi coagulation, kokucindezelwa ka ihlule legazi.

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